Figure 10.

Figure 10.

Recommended evaluations for gastrointestinal issues in individuals with fibrous dysplasia / McCune-Albright syndrome

GERD = gastroesophageal reflux disease; GI = gastrointestinal; H&P = history and physical examination; MAS = McCune-Albright syndrome; MRCP = magnetic resonance cholangiopancreatography; MRI = magnetic resonance imaging

1. To be performed at initial presentation in all individuals with MAS, regardless of clinical symptoms.

2. Age is not based upon clinical evidence, but on age at which affected individuals may undergo MRI/MRCP without requiring sedation, and should be individualized based on clinical judgment.

3. Age of onset of pancreatic cyst development is not established; therefore, clinical monitoring for gastrointestinal symptoms in these affected individuals is indicated.

4. Affected individuals should continue to be monitored clinically for new signs of gastrointestinal/pancreatic involvement, including pancreatitis and diabetes [Gaujoux et al 2014, Parvanescu et al 2014, Wood et al 2017].

From: Fibrous Dysplasia / McCune-Albright Syndrome

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