Table 2.

Lipoid Proteinosis: Frequency of Select Features

FeatureFrequency
In nearly allCommonInfrequent
Hoarse voice●
Severe dysphonia &/or complete aphonia●
Breathing difficulties●
Recurrent parotitis●
Poor dental health●
Thickened sublingual frenulum●
Vesicles & hemorrhagic crusts●
Moniliform blepharosis●
Hyperkeratotic & verrucous lesions●
Patchy & diffuse alopecia●
Epilepsy●
Neuropsychiatric disorders●
Spontaneous CNS hemorrhage●
Gastrointestinal bleeding●

From: Lipoid Proteinosis

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