Frontotemporal dementia
- Synonyms
- Dementia, frontotemporal, with or without parkinsonism; Dementia, frontotemporal, with parkinsonism; FRONTOTEMPORAL LOBAR DEGENERATION WITH TAU INCLUSIONS; FRONTOTEMPORAL LOBE DEMENTIA; FTLD WITH TAU INCLUSIONS; Frontotemporal lobe dementia (FLDEM); Multiple system tauopathy with presenile dementia; WILHELMSEN-LYNCH DISEASE; frontotemporal dementia with parkinsonism-17
- Modes of inheritance
- Autosomal dominant inheritance (Orphanet)
Summary
Available tests
Check Related conditions for additional relevant tests.
Clinical features
Help- Abnormality of the nervous system
- Abnormal sexual behavior
Abnormal sexual behavior
- MedGen UID: 99179
- Concept ID: C0474420
- Finding: Finding
Abnormality of the nervous system
- Amyotrophic lateral sclerosis
Amyotrophic lateral sclerosis
- MedGen UID: 274
- Concept ID: C0002736
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Apathy
Apathy
- MedGen UID: 39083
- Concept ID: C0085632
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Dementia
Dementia
- MedGen UID: 99229
- Concept ID: C0497327
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Diminished motivation
Diminished motivation
- MedGen UID: 96830
- Concept ID: C0456814
- Finding: Finding
Abnormality of the nervous system
- Frontal lobe dementia
Frontal lobe dementia
- MedGen UID: 572577
- Concept ID: C0338455
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Frontotemporal dementia
Frontotemporal dementia
- MedGen UID: 83266
- Concept ID: C0338451
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Hyperorality
Hyperorality
- MedGen UID: 325386
- Concept ID: C1838320
- Finding: Finding
Abnormality of the nervous system
- Impulse control disorder
Impulse control disorder
- MedGen UID: 5769
- Concept ID: C0021122
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Inappropriate laughter
Inappropriate laughter
- MedGen UID: 98407
- Concept ID: C0424304
- Finding: Finding
Abnormality of the nervous system
- Irritability
Irritability
- MedGen UID: 397841
- Concept ID: C2700617
- Finding: Mental Process
Abnormality of the nervous system
- Language disorder
Language disorder
- MedGen UID: 44069
- Concept ID: C0023015
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Neuronal loss in central nervous system
Neuronal loss in central nervous system
- MedGen UID: 342515
- Concept ID: C1850496
- Finding: Finding
Abnormality of the nervous system
- Parkinsonian disorder
Parkinsonian disorder
- MedGen UID: 66079
- Concept ID: C0242422
- Finding: Disease or Syndrome
Abnormality of the nervous system
- Personality changes
Personality changes
- MedGen UID: 66817
- Concept ID: C0240735
- Finding: Mental or Behavioral Dysfunction
Abnormality of the nervous system
- Polyphagia
Polyphagia
- MedGen UID: 9369
- Concept ID: C0020505
- Finding: Finding
Abnormality of the nervous system
- Primitive reflex
Primitive reflex
- MedGen UID: 333065
- Concept ID: C1838319
- Finding: Finding
Abnormality of the nervous system
- Abnormal sexual behavior
- NICE, 2023UK NICE Clinical guideline (CG148), Urinary incontinence in neurological disease: assessment and management, 2023
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