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Abnormal atrioventricular valve physiology

MedGen UID:
1647733
•Concept ID:
C4703462
•
Pathologic Function
HPO: HP:0031650

Definition

Any functional defect of the mitral or tricuspid valve. [from HPO]

Professional guidelines

PubMed

Prenatal Diagnosis and Management of Single-Ventricle Heart Disease.
Freud LR, Seed M
Can J Cardiol 2022 Jul;38(7):897-908. Epub 2022 Apr 13 doi: 10.1016/j.cjca.2022.04.003. PMID: 35429589
Management of the adult Fontan patient.
Rodriguez FH, Book WM
Heart 2020 Jan;106(2):105-110. Epub 2019 Oct 29 doi: 10.1136/heartjnl-2019-314937. PMID: 31662332
Postnatal Outcome Following Prenatal Diagnosis of Discordant Atrioventricular and Ventriculoarterial Connections.
Day TG, Woodgate T, Knee O, Zidere V, Vigneswaran T, Charakida M, Miller O, Sharland G, Simpson J
Pediatr Cardiol 2019 Oct;40(7):1509-1515. Epub 2019 Jul 25 doi: 10.1007/s00246-019-02176-2. PMID: 31342118

Recent clinical studies

Etiology

Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Surgical Considerations in Atrioventricular Canal Defects.
Malik M, Khalid Nuri M
Semin Cardiothorac Vasc Anesth 2017 Sep;21(3):229-234. Epub 2017 May 8 doi: 10.1177/1089253217708622. PMID: 28482733
Pitfalls in repair of conotruncal anomalies.
Raisky O, Vouhé PR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):7-12. doi: 10.1053/j.pcsu.2013.02.001. PMID: 23561812
Bridging annuloplasty for left atrioventricular valve of partial atrioventricular septal defect.
Aeba R, Kudo M, Okamoto K, Yozu R
Ann Thorac Surg 2012 May;93(5):e137-9. doi: 10.1016/j.athoracsur.2011.12.071. PMID: 22541239
Role of ablation therapy in ventricular arrhythmias.
Das MK, Dandamudi G, Steiner H
Cardiol Clin 2008 Aug;26(3):459-79, vii. doi: 10.1016/j.ccl.2008.03.010. PMID: 18538191

Diagnosis

Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Clinical significance of conduction disturbances after aortic valve intervention: current evidence.
Martinez-Selles M, Bramlage P, Thoenes M, Schymik G
Clin Res Cardiol 2015 Jan;104(1):1-12. Epub 2014 Jul 4 doi: 10.1007/s00392-014-0739-6. PMID: 24990451
Pitfalls in repair of conotruncal anomalies.
Raisky O, Vouhé PR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):7-12. doi: 10.1053/j.pcsu.2013.02.001. PMID: 23561812
Clapping atrio-ventricular valves.
Senguttuvan NB, Goswami KC
Heart 2013 Aug;99(15):1140. Epub 2012 Aug 15 doi: 10.1136/heartjnl-2012-302710. PMID: 22895642
Tricuspid regurgitation: pathophysiology and management.
Thapa R, Dawn B, Nath J
Curr Cardiol Rep 2012 Apr;14(2):190-9. doi: 10.1007/s11886-012-0245-2. PMID: 22350692

Therapy

ADO II in Percutaneous VSD Closure in Pediatric Patients.
Narin N, Baykan A, Pamukcu O, Argun M, Ozyurt A, Mese T, Yilmazer MM, Gunes I, Kazım U
J Interv Cardiol 2015 Oct;28(5):479-84. Epub 2015 Sep 8 doi: 10.1111/joic.12222. PMID: 26345701
Clinical significance of conduction disturbances after aortic valve intervention: current evidence.
Martinez-Selles M, Bramlage P, Thoenes M, Schymik G
Clin Res Cardiol 2015 Jan;104(1):1-12. Epub 2014 Jul 4 doi: 10.1007/s00392-014-0739-6. PMID: 24990451
Pitfalls in repair of conotruncal anomalies.
Raisky O, Vouhé PR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):7-12. doi: 10.1053/j.pcsu.2013.02.001. PMID: 23561812
Bridging annuloplasty for left atrioventricular valve of partial atrioventricular septal defect.
Aeba R, Kudo M, Okamoto K, Yozu R
Ann Thorac Surg 2012 May;93(5):e137-9. doi: 10.1016/j.athoracsur.2011.12.071. PMID: 22541239
Evaluation and management of the adult patient with transposition of the great arteries following atrial-level (Senning or Mustard) repair.
Love BA, Mehta D, Fuster VF
Nat Clin Pract Cardiovasc Med 2008 Aug;5(8):454-67. Epub 2008 Jul 1 doi: 10.1038/ncpcardio1252. PMID: 18594551

Prognosis

Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Management of the adult Fontan patient.
Rodriguez FH, Book WM
Heart 2020 Jan;106(2):105-110. Epub 2019 Oct 29 doi: 10.1136/heartjnl-2019-314937. PMID: 31662332
Pitfalls in repair of conotruncal anomalies.
Raisky O, Vouhé PR
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2013;16(1):7-12. doi: 10.1053/j.pcsu.2013.02.001. PMID: 23561812
Bridging annuloplasty for left atrioventricular valve of partial atrioventricular septal defect.
Aeba R, Kudo M, Okamoto K, Yozu R
Ann Thorac Surg 2012 May;93(5):e137-9. doi: 10.1016/j.athoracsur.2011.12.071. PMID: 22541239
Congenitally corrected transposition.
Wallis GA, Debich-Spicer D, Anderson RH
Orphanet J Rare Dis 2011 May 14;6:22. doi: 10.1186/1750-1172-6-22. PMID: 21569592Free PMC Article

Clinical prediction guides

Ex Vivo Modeling of Atrioventricular Valve Mechanics in Single Ventricle Physiology.
Moye SC, Kidambi S, Lee JY, Cowles TH, Gilligan-Steinberg SD, Bryan AY, Wilkerson R, Woo YJ, Ma MR
Ann Biomed Eng 2023 Aug;51(8):1738-1746. Epub 2023 Mar 25 doi: 10.1007/s10439-023-03178-1. PMID: 36966247Free PMC Article
Anterior Tricuspid Leaflet Cleft in an Adult Male: An Autopsy Case Report.
Yamasaki G, Kondo T, Kuse A, Sugimoto M, Takahashi M, Morichika M, Nakagawa K, Sakurada M, Asano M, Ueno Y
Am J Forensic Med Pathol 2020 Mar;41(1):40-41. doi: 10.1097/PAF.0000000000000525. PMID: 31929320
Diagnosis of major heart defects by routine first-trimester ultrasound examination: association with increased nuchal translucency, tricuspid regurgitation and abnormal flow in ductus venosus.
Minnella GP, Crupano FM, Syngelaki A, Zidere V, Akolekar R, Nicolaides KH
Ultrasound Obstet Gynecol 2020 May;55(5):637-644. doi: 10.1002/uog.21956. PMID: 31875326
Utility of expert focused cardiac ultrasound in paediatric cardiology outreach clinics.
Rauser-Foltz KK, Danford DA, Strawn JK, Kutty S
Cardiol Young 2019 Dec;29(12):1468-1473. Epub 2019 Nov 18 doi: 10.1017/S1047951119002427. PMID: 31735194
Surgical strategy for aortic arch reconstruction after the Norwood procedure based on numerical flow analysis.
Miyazaki S, Miyaji K, Itatani K, Oka N, Goto S, Nakamura M, Kitamura T, Horai T, Sughimoto K, Nakamura Y, Yoshimura N
Interact Cardiovasc Thorac Surg 2018 Mar 1;26(3):460-467. doi: 10.1093/icvts/ivx332. PMID: 29049796

Recent systematic reviews

Risk factors for death or heart transplantation in single-ventricle physiology (tricuspid atresia, pulmonary atresia, and heterotaxy): A systematic review and meta-analysis.
Kulkarni A, Patel N, Singh TP, Mossialos E, Mehra MR
J Heart Lung Transplant 2019 Jul;38(7):739-747. Epub 2019 Apr 4 doi: 10.1016/j.healun.2019.04.001. PMID: 31006521
Predicting long-term mortality after Fontan procedures: A risk score based on 6707 patients from 28 studies.
Alsaied T, Bokma JP, Engel ME, Kuijpers JM, Hanke SP, Zuhlke L, Zhang B, Veldtman GR
Congenit Heart Dis 2017 Jul;12(4):393-398. Epub 2017 May 8 doi: 10.1111/chd.12468. PMID: 28480627

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