U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Paratesticular Rhabdomyosarcoma

MedGen UID:
1695863
•Concept ID:
C5206600
•
Neoplastic Process

Definition

A rhabdomyosarcoma that arises from the paratesticular region. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVParatesticular Rhabdomyosarcoma

Professional guidelines

PubMed

Surgical management of paratesticular rhabdomyosarcoma: A consensus opinion from the Children's Oncology Group, European paediatric Soft tissue sarcoma Study Group, and the Cooperative Weichteilsarkom Studiengruppe.
Rogers TN, Seitz G, Fuchs J, Martelli H, Dasgupta R, Routh JC, Hawkins DS, Koscielniak E, Bisogno G, Rodeberg DA
Pediatr Blood Cancer 2021 Apr;68(4):e28938. Epub 2021 Feb 1 doi: 10.1002/pbc.28938. PMID: 33522706Free PMC Article
Outcome, Treatment, and Treatment Failures in Patients Suffering Localized Embryonal Paratesticular Rhabdomyosarcoma: Results From the "Cooperative Weichteilsarkom Studiengruppe" Trials CWS-86, -91, -96, and -2002P.
Seitz G, Fuchs J, Martus P, Klingebiel T, Leuschner I, Schuck A, Dantonello TM, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe (CWS).
Ann Surg 2016 Dec;264(6):1148-1155. doi: 10.1097/SLA.0000000000001550. PMID: 27828824
Paratesticular rhabdomyosarcoma: delayed effects of multimodality therapy and implications for current management.
Hughes LL, Baruzzi MJ, Ribeiro RC, Ayers GD, Rao B, Parham DM, Pratt CB, Kun LE
Cancer 1994 Jan 15;73(2):476-82. doi: 10.1002/1097-0142(19940115)73:2<476::aid-cncr2820730237>3.0.co;2-n. PMID: 8293416

Recent clinical studies

Etiology

Malignant testicular tumors in children: A single institution's 12-year experience.
Chiu CC, Jaing TH, Lai JY, Chen SH, Chang TY, Hsueh C, Wen YC, Tsay PK
Medicine (Baltimore) 2022 Jul 22;101(29):e29735. doi: 10.1097/MD.0000000000029735. PMID: 35866814Free PMC Article
Update on pediatric rhabdomyosarcoma: A report from the APSA Cancer Committee.
Rhee DS, Rodeberg DA, Baertschiger RM, Aldrink JH, Lautz TB, Grant C, Meyers RL, Tracy ET, Christison-Lagay ER, Glick RD, Mattei P, Dasgupta R; American Pediatric Surgical Association Cancer Committee
J Pediatr Surg 2020 Oct;55(10):1987-1995. Epub 2020 Jun 18 doi: 10.1016/j.jpedsurg.2020.06.015. PMID: 32674846
Paratesticular alveolar rhabdomyosarcomas do not harbor typical translocations: a distinct entity with favorable prognosis?
Dantonello TM, Vokuhl C, Scheer M, Sparber-Sauer M, Stegmaier S, Seitz G, Scheithauer H, Faber J, Veit-Friedrich I, Kaatsch P, Bielack SS, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe (CWS)
Virchows Arch 2018 Mar;472(3):441-449. Epub 2018 Feb 21 doi: 10.1007/s00428-018-2311-7. PMID: 29468306
Paratesticular rhabdomyosarcoma.
de Vries JD
World J Urol 1995;13(4):219-25. doi: 10.1007/BF00182966. PMID: 8528295
Paratesticular rhabdomyosarcoma: delayed effects of multimodality therapy and implications for current management.
Hughes LL, Baruzzi MJ, Ribeiro RC, Ayers GD, Rao B, Parham DM, Pratt CB, Kun LE
Cancer 1994 Jan 15;73(2):476-82. doi: 10.1002/1097-0142(19940115)73:2<476::aid-cncr2820730237>3.0.co;2-n. PMID: 8293416

Diagnosis

Malignant testicular tumors in children: A single institution's 12-year experience.
Chiu CC, Jaing TH, Lai JY, Chen SH, Chang TY, Hsueh C, Wen YC, Tsay PK
Medicine (Baltimore) 2022 Jul 22;101(29):e29735. doi: 10.1097/MD.0000000000029735. PMID: 35866814Free PMC Article
Paratesticular alveolar rhabdomyosarcomas do not harbor typical translocations: a distinct entity with favorable prognosis?
Dantonello TM, Vokuhl C, Scheer M, Sparber-Sauer M, Stegmaier S, Seitz G, Scheithauer H, Faber J, Veit-Friedrich I, Kaatsch P, Bielack SS, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe (CWS)
Virchows Arch 2018 Mar;472(3):441-449. Epub 2018 Feb 21 doi: 10.1007/s00428-018-2311-7. PMID: 29468306
Paratesticular rhabdomyosarcoma.
de Vries JD
World J Urol 1995;13(4):219-25. doi: 10.1007/BF00182966. PMID: 8528295
Paratesticular rhabdomyosarcoma (RMS) and paraaortic lymphadenectomy.
Gamba PG, Cecchetto G, Katende M, Carli M, Sotti G, Guglielmi M
Eur J Pediatr Surg 1994 Jun;4(3):158-60. doi: 10.1055/s-2008-1066091. PMID: 8086392
Genitourinary rhabdomyosarcoma.
Kaplan WE, Firlit CF, Berger RM
J Urol 1983 Jul;130(1):116-9. doi: 10.1016/s0022-5347(17)50987-8. PMID: 6864889

Therapy

Pediatric genitourinary tumors.
Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
Paratesticular rhabdomyosarcoma (RMS) and paraaortic lymphadenectomy.
Gamba PG, Cecchetto G, Katende M, Carli M, Sotti G, Guglielmi M
Eur J Pediatr Surg 1994 Jun;4(3):158-60. doi: 10.1055/s-2008-1066091. PMID: 8086392
Late effects of therapy in patients with paratesticular rhabdomyosarcoma. Intergroup Rhabdomyosarcoma Study Committee.
Heyn R, Raney RB Jr, Hays DM, Tefft M, Gehan E, Webber B, Maurer HM
J Clin Oncol 1992 Apr;10(4):614-23. doi: 10.1200/JCO.1992.10.4.614. PMID: 1548524
Genitourinary rhabdomyosarcoma.
Kaplan WE, Firlit CF, Berger RM
J Urol 1983 Jul;130(1):116-9. doi: 10.1016/s0022-5347(17)50987-8. PMID: 6864889
Paratesticular rhabdomyosarcoma in childhood.
Raney RB Jr, Hays DM, Lawrence W Jr, Soule EH, Tefft M, Donaldson MH
Cancer 1978 Aug;42(2):729-36. doi: 10.1002/1097-0142(197808)42:2<729::aid-cncr2820420246>3.0.co;2-r. PMID: 354776

Prognosis

Impact of local control and surgical lymph node evaluation in localized paratesticular rhabdomyosarcoma: A report from the Children's Oncology Group Soft Tissue Sarcoma Committee.
Routh JC, Dasgupta R, Chi YY, Shnorhavorian M, Tian J, Walterhouse DO, Breneman J, Wolden SL, Arndt CA, Hawkins DS, Rodeberg DA
Int J Cancer 2020 Dec 1;147(11):3168-3176. Epub 2020 Jul 11 doi: 10.1002/ijc.33143. PMID: 32525556Free PMC Article
Paratesticular alveolar rhabdomyosarcomas do not harbor typical translocations: a distinct entity with favorable prognosis?
Dantonello TM, Vokuhl C, Scheer M, Sparber-Sauer M, Stegmaier S, Seitz G, Scheithauer H, Faber J, Veit-Friedrich I, Kaatsch P, Bielack SS, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe (CWS)
Virchows Arch 2018 Mar;472(3):441-449. Epub 2018 Feb 21 doi: 10.1007/s00428-018-2311-7. PMID: 29468306
Paratesticular rhabdomyosarcoma.
de Vries JD
World J Urol 1995;13(4):219-25. doi: 10.1007/BF00182966. PMID: 8528295
Paratesticular rhabdomyosarcoma: delayed effects of multimodality therapy and implications for current management.
Hughes LL, Baruzzi MJ, Ribeiro RC, Ayers GD, Rao B, Parham DM, Pratt CB, Kun LE
Cancer 1994 Jan 15;73(2):476-82. doi: 10.1002/1097-0142(19940115)73:2<476::aid-cncr2820730237>3.0.co;2-n. PMID: 8293416
Paratesticular rhabdomyosarcoma in childhood.
Raney RB Jr, Hays DM, Lawrence W Jr, Soule EH, Tefft M, Donaldson MH
Cancer 1978 Aug;42(2):729-36. doi: 10.1002/1097-0142(197808)42:2<729::aid-cncr2820420246>3.0.co;2-r. PMID: 354776

Clinical prediction guides

Primary intratesticular rhabdomyosarcoma, a rare entity: A case report with review of literature.
Lachi PK, Armugham N, Triveni B, Sheela B, Krishna MR
J Cancer Res Ther 2021 Apr-Jun;17(2):590-592. doi: 10.4103/jcrt.JCRT_585_15. PMID: 34121716
Epidemiologic study of 230 cases of testicular/paratesticular tumors or masses: 15-year experience of a single center.
Shen J, Bi Y, Wang X, Lu L, Tang L, Liu Y, Chen H, Zhang B
J Pediatr Surg 2017 Dec;52(12):2056-2060. Epub 2017 Sep 4 doi: 10.1016/j.jpedsurg.2017.08.027. PMID: 28967388
Paratesticular rhabdomyosarcoma: Importance of initial therapy.
Hammond WJ, Farber BA, Price AP, Wolden SL, Heaton TE, Wexler LH, La Quaglia MP
J Pediatr Surg 2017 Feb;52(2):304-308. Epub 2016 Nov 14 doi: 10.1016/j.jpedsurg.2016.11.027. PMID: 27894767Free PMC Article
Pediatric genitourinary tumors.
Merguerian PA, Chang B
Curr Opin Oncol 2002 May;14(3):273-9. doi: 10.1097/00001622-200205000-00004. PMID: 11981271
Paratesticular rhabdomyosarcoma (RMS) and paraaortic lymphadenectomy.
Gamba PG, Cecchetto G, Katende M, Carli M, Sotti G, Guglielmi M
Eur J Pediatr Surg 1994 Jun;4(3):158-60. doi: 10.1055/s-2008-1066091. PMID: 8086392

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...