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Abnormal arcuate artery morphology

MedGen UID:
1784522
•Concept ID:
C5539842
•
Anatomical Abnormality
Synonym: Abnormalities of arcuate arteries
 
HPO: HP:0033837

Definition

Anomalous structure of the arc-shaped arteries located at the border of the renal cortex and renal medulla. [from HPO]

Professional guidelines

PubMed

The presentation and management of aneurysms of the pancreaticoduodenal arcade.
Corey MR, Ergul EA, Cambria RP, Patel VI, Lancaster RT, Kwolek CJ, Conrad MF
J Vasc Surg 2016 Dec;64(6):1734-1740. doi: 10.1016/j.jvs.2016.05.067. PMID: 27871496
Contemporary management of median arcuate ligament syndrome provides early symptom improvement.
Columbo JA, Trus T, Nolan B, Goodney P, Rzucidlo E, Powell R, Walsh D, Stone D
J Vasc Surg 2015 Jul;62(1):151-6. Epub 2015 Mar 7 doi: 10.1016/j.jvs.2015.01.050. PMID: 25758451Free PMC Article

Recent clinical studies

Etiology

Vascular compression syndromes in the abdomen and pelvis: a concise pictorial review.
M Koshy R, Chee RKW, Wilson MP, Singh R, Mathew RP, Tu W, Low G
Abdom Radiol (NY) 2024 May;49(5):1747-1761. Epub 2024 Apr 29 doi: 10.1007/s00261-024-04315-7. PMID: 38683215
New insights into the etiopathology of placenta accreta spectrum.
Jauniaux E, Jurkovic D, Hussein AM, Burton GJ
Am J Obstet Gynecol 2022 Sep;227(3):384-391. Epub 2022 Mar 3 doi: 10.1016/j.ajog.2022.02.038. PMID: 35248577
Pathophysiology of Placenta Accreta Spectrum Disorders: A Review of Current Findings.
Jauniaux E, Burton GJ
Clin Obstet Gynecol 2018 Dec;61(4):743-754. doi: 10.1097/GRF.0000000000000392. PMID: 30299280
Median Arcuate Ligament Syndrome: A Single-Center Experience with 23 Patients.
Nasr LA, Faraj WG, Al-Kutoubi A, Hamady M, Khalifeh M, Hallal A, Halawani HM, Wazen J, Haydar AA
Cardiovasc Intervent Radiol 2017 May;40(5):664-670. Epub 2017 Jan 3 doi: 10.1007/s00270-016-1560-6. PMID: 28050657
CT angiography of the celiac trunk: anatomy, variants and pathologic findings.
Ozbülbül NI
Diagn Interv Radiol 2011 Jun;17(2):150-7. Epub 2010 Aug 6 doi: 10.4261/1305-3825.DIR.3283-10.1. PMID: 20690078

Diagnosis

Vascular compression syndromes in the abdomen and pelvis: a concise pictorial review.
M Koshy R, Chee RKW, Wilson MP, Singh R, Mathew RP, Tu W, Low G
Abdom Radiol (NY) 2024 May;49(5):1747-1761. Epub 2024 Apr 29 doi: 10.1007/s00261-024-04315-7. PMID: 38683215
Chronic Abdominal Pain, an Overlooked Diagnosis of Median Arcuate Ligament Syndrome (MALS).
Nikolova D, Antovic S, Karagjozov P, Kitevski V, Trajkovska M, Dimitrova MG, Deriban G, Trpcevska EN, Nikolovska AV
Pril (Makedon Akad Nauk Umet Odd Med Nauki) 2022 Apr 22;43(1):95-99. doi: 10.2478/prilozi-2022-0009. PMID: 35451292
Postprandial Abdominal Pain.
Yoon DY, Nemcek AA, Kibbe MR
JAMA Surg 2016 Mar;151(3):287-8. doi: 10.1001/jamasurg.2015.4715. PMID: 26792420
Median arcuate ligament compression of the mesenteric vasculature.
Tracci MC
Tech Vasc Interv Radiol 2015 Mar;18(1):43-50. Epub 2014 Dec 29 doi: 10.1053/j.tvir.2014.12.007. PMID: 25814203
Index of suspicion.
Ostrom K, Syan R, Barber L, Miller D, Venkatasubramani N, Ravindra A, Jhaveri P, Jhaveri P, Alexander C, Nagan MR, Hauptman M, Grover A, Hadland SE
Pediatr Rev 2014 Sep;35(9):396-404. doi: 10.1542/pir.35-9-396. PMID: 25183775

Therapy

Pancreaticoduodenectomy combined gastroduodenal collateral reconstruction and preservation due to median arcuate ligament syndrome: technical notes with two surgical cases report (with video).
Nguyen TK, Nguyen HH, Luong TH, Chantha P, Ngo GK, Le VD, Dang KK, Tran DH, Nguyen CT
World J Surg Oncol 2023 Jul 17;21(1):206. doi: 10.1186/s12957-023-03096-5. PMID: 37461042Free PMC Article
Chronic Abdominal Pain, an Overlooked Diagnosis of Median Arcuate Ligament Syndrome (MALS).
Nikolova D, Antovic S, Karagjozov P, Kitevski V, Trajkovska M, Dimitrova MG, Deriban G, Trpcevska EN, Nikolovska AV
Pril (Makedon Akad Nauk Umet Odd Med Nauki) 2022 Apr 22;43(1):95-99. doi: 10.2478/prilozi-2022-0009. PMID: 35451292
The presentation and management of aneurysms of the pancreaticoduodenal arcade.
Corey MR, Ergul EA, Cambria RP, Patel VI, Lancaster RT, Kwolek CJ, Conrad MF
J Vasc Surg 2016 Dec;64(6):1734-1740. doi: 10.1016/j.jvs.2016.05.067. PMID: 27871496
Dunbar syndrome following liver transplantation.
Ali M, Patel J
BMJ Case Rep 2016 Feb 8;2016 doi: 10.1136/bcr-2015-214168. PMID: 26857586Free PMC Article
Median arcuate ligament compression of the mesenteric vasculature.
Tracci MC
Tech Vasc Interv Radiol 2015 Mar;18(1):43-50. Epub 2014 Dec 29 doi: 10.1053/j.tvir.2014.12.007. PMID: 25814203

Prognosis

Laparoscopic approach to median arcuate ligament syndrome (with video).
Landen S, Ballet T, Delugeau V, Landen C
J Visc Surg 2018 Apr;155(2):159-161. Epub 2018 Apr 17 doi: 10.1016/j.jviscsurg.2017.12.014. PMID: 29678321
Median Arcuate Ligament Syndrome: A Single-Center Experience with 23 Patients.
Nasr LA, Faraj WG, Al-Kutoubi A, Hamady M, Khalifeh M, Hallal A, Halawani HM, Wazen J, Haydar AA
Cardiovasc Intervent Radiol 2017 May;40(5):664-670. Epub 2017 Jan 3 doi: 10.1007/s00270-016-1560-6. PMID: 28050657
Median arcuate ligament syndrome confirmed with the use of intravascular ultrasound.
de Lara FV, Higgins C, Hernandez-Vila EA
Tex Heart Inst J 2014 Feb;41(1):57-60. doi: 10.14503/THIJ-12-2495. PMID: 24512402Free PMC Article
Pancreaticoduodenal artery aneurysm associated with median arcuate ligament syndrome.
Armstrong MB, Stadtlander KS, Grove MK
Ann Vasc Surg 2014 Apr;28(3):741.e1-5. Epub 2013 Oct 24 doi: 10.1016/j.avsg.2013.06.030. PMID: 24495330
Celiac artery compression syndrome: a radiological finding without clinical symptoms?
Kazan V, Qu W, Al-Natour M, Abbas J, Nazzal M
Vascular 2013 Oct;21(5):293-9. Epub 2013 May 7 doi: 10.1177/1708538113478750. PMID: 23508388

Clinical prediction guides

Pancreaticoduodenectomy combined gastroduodenal collateral reconstruction and preservation due to median arcuate ligament syndrome: technical notes with two surgical cases report (with video).
Nguyen TK, Nguyen HH, Luong TH, Chantha P, Ngo GK, Le VD, Dang KK, Tran DH, Nguyen CT
World J Surg Oncol 2023 Jul 17;21(1):206. doi: 10.1186/s12957-023-03096-5. PMID: 37461042Free PMC Article
An unusual case of left renal artery compression: a rare type of median arcuate ligament syndrome.
Arazińska A, Polguj M, Wojciechowski A, Trębiński Ł, Stefańczyk L
Surg Radiol Anat 2016 Apr;38(3):379-82. Epub 2015 May 5 doi: 10.1007/s00276-015-1478-8. PMID: 25940812Free PMC Article
Vascular compression syndromes.
Czihal M, Banafsche R, Hoffmann U, Koeppel T
Vasa 2015 Nov;44(6):419-34. doi: 10.1024/0301-1526/a000465. PMID: 26515219
Median arcuate ligament syndrome confirmed with the use of intravascular ultrasound.
de Lara FV, Higgins C, Hernandez-Vila EA
Tex Heart Inst J 2014 Feb;41(1):57-60. doi: 10.14503/THIJ-12-2495. PMID: 24512402Free PMC Article
Celiac artery compression syndrome: a radiological finding without clinical symptoms?
Kazan V, Qu W, Al-Natour M, Abbas J, Nazzal M
Vascular 2013 Oct;21(5):293-9. Epub 2013 May 7 doi: 10.1177/1708538113478750. PMID: 23508388

Recent systematic reviews

Characteristics and Trends in Median Arcuate Ligament Syndrome (MALS) Associated Visceral Artery Aneurysms: A Systematic Descriptive Review of the Literature.
Karanasios E, Ragab Z, Cavenagh H, Stather P, Ali T
Vasc Endovascular Surg 2024 Jul;58(5):512-522. Epub 2024 Jan 25 doi: 10.1177/15385744241229842. PMID: 38271562

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