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Idiopathic steroid-resistant nephrotic syndrome with sensitivity to second-line immunosuppressive therapy

MedGen UID:
1842217
•Concept ID:
C5680133
•
Disease or Syndrome
Synonyms: Idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression; idiopathic steroid-resistant nephrotic syndrome with sensitivity to intensified immunosuppression; idiopathic steroid-resistant nephrotic syndrome with sensitivity to second-line immunosuppressive therapy
 
Monarch Initiative: MONDO:0035460
Orphanet: ORPHA567552

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVIdiopathic steroid-resistant nephrotic syndrome with sensitivity to second-line immunosuppressive therapy

Recent clinical studies

Etiology

Long-term follow-up after cyclophosphamide and cyclosporine-A therapy in steroid-dependent and -resistant nephrotic syndrome.
Sümegi V, Haszon I, Bereczki C, Papp F, Túri S
Pediatr Nephrol 2008 Jul;23(7):1085-92. Epub 2008 Mar 7 doi: 10.1007/s00467-008-0771-8. PMID: 18324421

Diagnosis

Childhood nephrotic syndrome.
Vivarelli M, Gibson K, Sinha A, Boyer O
Lancet 2023 Sep 2;402(10404):809-824. doi: 10.1016/S0140-6736(23)01051-6. PMID: 37659779
Minimal Change Disease.
Vivarelli M, Massella L, Ruggiero B, Emma F
Clin J Am Soc Nephrol 2017 Feb 7;12(2):332-345. Epub 2016 Dec 9 doi: 10.2215/CJN.05000516. PMID: 27940460Free PMC Article
Long-term follow-up after cyclophosphamide and cyclosporine-A therapy in steroid-dependent and -resistant nephrotic syndrome.
Sümegi V, Haszon I, Bereczki C, Papp F, Túri S
Pediatr Nephrol 2008 Jul;23(7):1085-92. Epub 2008 Mar 7 doi: 10.1007/s00467-008-0771-8. PMID: 18324421

Therapy

Childhood nephrotic syndrome.
Vivarelli M, Gibson K, Sinha A, Boyer O
Lancet 2023 Sep 2;402(10404):809-824. doi: 10.1016/S0140-6736(23)01051-6. PMID: 37659779
Minimal Change Disease.
Vivarelli M, Massella L, Ruggiero B, Emma F
Clin J Am Soc Nephrol 2017 Feb 7;12(2):332-345. Epub 2016 Dec 9 doi: 10.2215/CJN.05000516. PMID: 27940460Free PMC Article
Long-term follow-up after cyclophosphamide and cyclosporine-A therapy in steroid-dependent and -resistant nephrotic syndrome.
Sümegi V, Haszon I, Bereczki C, Papp F, Túri S
Pediatr Nephrol 2008 Jul;23(7):1085-92. Epub 2008 Mar 7 doi: 10.1007/s00467-008-0771-8. PMID: 18324421

Prognosis

Childhood nephrotic syndrome.
Vivarelli M, Gibson K, Sinha A, Boyer O
Lancet 2023 Sep 2;402(10404):809-824. doi: 10.1016/S0140-6736(23)01051-6. PMID: 37659779
Long-term follow-up after cyclophosphamide and cyclosporine-A therapy in steroid-dependent and -resistant nephrotic syndrome.
Sümegi V, Haszon I, Bereczki C, Papp F, Túri S
Pediatr Nephrol 2008 Jul;23(7):1085-92. Epub 2008 Mar 7 doi: 10.1007/s00467-008-0771-8. PMID: 18324421

Clinical prediction guides

Childhood nephrotic syndrome.
Vivarelli M, Gibson K, Sinha A, Boyer O
Lancet 2023 Sep 2;402(10404):809-824. doi: 10.1016/S0140-6736(23)01051-6. PMID: 37659779

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