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Congenital disorder of glycosylation with skin involvement

MedGen UID:
1842264
Concept ID:
C5680020
Disease or Syndrome
Synonym: CDG with skin involvement
 
Orphanet: ORPHA371200

Recent clinical studies

Etiology

Picker SM, Parker G, Gissen P
Int J Mol Sci 2023 Aug 31;24(17) doi: 10.3390/ijms241713545. PMID: 37686358Free PMC Article
Linders PTA, Peters E, Ter Beest M, Lefeber DJ, van den Bogaart G
Int J Mol Sci 2020 Jun 30;21(13) doi: 10.3390/ijms21134654. PMID: 32629928Free PMC Article
Lamari F, Mochel F, Saudubray JM
J Inherit Metab Dis 2015 Jan;38(1):3-18. Epub 2014 Sep 20 doi: 10.1007/s10545-014-9764-x. PMID: 25238787
Yang L, Fliegauf M, Grimbacher B
Curr Opin Pediatr 2014 Dec;26(6):697-703. doi: 10.1097/MOP.0000000000000158. PMID: 25365149
Rymen D, Jaeken J
J Inherit Metab Dis 2014 Sep;37(5):699-708. Epub 2014 Feb 20 doi: 10.1007/s10545-014-9678-7. PMID: 24554337

Diagnosis

Zhao P, Zhang L, Tan L, Luo S, Huang Y, Peng H, Cao J, He X
Mol Genet Genomic Med 2021 Sep;9(9):e1751. Epub 2021 Jul 31 doi: 10.1002/mgg3.1751. PMID: 34331832Free PMC Article
Linders PTA, Peters E, Ter Beest M, Lefeber DJ, van den Bogaart G
Int J Mol Sci 2020 Jun 30;21(13) doi: 10.3390/ijms21134654. PMID: 32629928Free PMC Article
Fischer J, Bourrat E
Acta Derm Venereol 2020 Mar 25;100(7):adv00096. doi: 10.2340/00015555-3432. PMID: 32147747Free PMC Article
Radke J, Stenzel W, Goebel HH
Handb Clin Neurol 2017;145:133-146. doi: 10.1016/B978-0-12-802395-2.00009-2. PMID: 28987164
Höck M, Wegleiter K, Ralser E, Kiechl-Kohlendorfer U, Scholl-Bürgi S, Fauth C, Steichen E, Pichler K, Lefeber DJ, Matthjis G, Keldermans L, Maurer K, Zschocke J, Karall D
Orphanet J Rare Dis 2015 Jun 12;10:73. doi: 10.1186/s13023-015-0289-7. PMID: 26066342Free PMC Article

Therapy

Pestronk A
J Neuropathol Exp Neurol 2020 Jan 1;79(1):102-112. doi: 10.1093/jnen/nlz111. PMID: 31803918
Morelle W, Potelle S, Witters P, Wong S, Climer L, Lupashin V, Matthijs G, Gadomski T, Jaeken J, Cassiman D, Morava E, Foulquier F
J Clin Endocrinol Metab 2017 Apr 1;102(4):1375-1386. doi: 10.1210/jc.2016-3443. PMID: 28323990Free PMC Article

Prognosis

Höck M, Wegleiter K, Ralser E, Kiechl-Kohlendorfer U, Scholl-Bürgi S, Fauth C, Steichen E, Pichler K, Lefeber DJ, Matthjis G, Keldermans L, Maurer K, Zschocke J, Karall D
Orphanet J Rare Dis 2015 Jun 12;10:73. doi: 10.1186/s13023-015-0289-7. PMID: 26066342Free PMC Article
Lamari F, Mochel F, Saudubray JM
J Inherit Metab Dis 2015 Jan;38(1):3-18. Epub 2014 Sep 20 doi: 10.1007/s10545-014-9764-x. PMID: 25238787
Kouwenberg D, Gardeitchik T, Mohamed M, Lefeber DJ, Morava E
Pediatr Dermatol 2014 Jan-Feb;31(1):e1-5. doi: 10.1111/pde.12233. PMID: 24555185
Morava E, Zeevaert R, Korsch E, Huijben K, Wopereis S, Matthijs G, Keymolen K, Lefeber DJ, De Meirleir L, Wevers RA
Eur J Hum Genet 2007 Jun;15(6):638-45. Epub 2007 Mar 14 doi: 10.1038/sj.ejhg.5201813. PMID: 17356545

Clinical prediction guides

Morelle W, Potelle S, Witters P, Wong S, Climer L, Lupashin V, Matthijs G, Gadomski T, Jaeken J, Cassiman D, Morava E, Foulquier F
J Clin Endocrinol Metab 2017 Apr 1;102(4):1375-1386. doi: 10.1210/jc.2016-3443. PMID: 28323990Free PMC Article
Lamari F, Mochel F, Saudubray JM
J Inherit Metab Dis 2015 Jan;38(1):3-18. Epub 2014 Sep 20 doi: 10.1007/s10545-014-9764-x. PMID: 25238787
Rymen D, Jaeken J
J Inherit Metab Dis 2014 Sep;37(5):699-708. Epub 2014 Feb 20 doi: 10.1007/s10545-014-9678-7. PMID: 24554337
Dupré T, Vuillaumier-Barrot S, Chantret I, Sadou Yayé H, Le Bizec C, Afenjar A, Altuzarra C, Barnérias C, Burglen L, de Lonlay P, Feillet F, Napuri S, Seta N, Moore SE
J Med Genet 2010 Nov;47(11):729-35. Epub 2010 Aug 2 doi: 10.1136/jmg.2009.072504. PMID: 20679665
Sturla L, Fruscione F, Noda K, Miyoshi E, Taniguchi N, Contini P, Tonetti M
Glycobiology 2005 Oct;15(10):924-34. Epub 2005 May 25 doi: 10.1093/glycob/cwi081. PMID: 15917429

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