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Central nervous system extraskeletal osteosarcoma

MedGen UID:
233803
•Concept ID:
C1335150
•
Neoplastic Process
Synonyms: Central Nervous System Extraskeletal Osteosarcoma; central nervous system extraskeletal osteosarcoma; central nervous system osteosarcoma; central nervous system osteosarcoma (disease); Osteosarcoma of Central Nervous System; osteosarcoma of central nervous system; Osteosarcoma of the Central Nervous System; osteosarcoma of the central nervous system
 
Monarch Initiative: MONDO:0004423

Definition

An osteosarcoma arising from the brain or spinal cord. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCentral nervous system extraskeletal osteosarcoma

Professional guidelines

PubMed

Sarcoma metastatic to the brain: results of surgical treatment.
Bindal RK, Sawaya RE, Leavens ME, Taylor SH, Guinee VF
Neurosurgery 1994 Aug;35(2):185-90; discussion 190-1. doi: 10.1227/00006123-199408000-00002. PMID: 7969824

Recent clinical studies

Etiology

Sarcoma metastatic to the brain: results of surgical treatment.
Bindal RK, Sawaya RE, Leavens ME, Taylor SH, Guinee VF
Neurosurgery 1994 Aug;35(2):185-90; discussion 190-1. doi: 10.1227/00006123-199408000-00002. PMID: 7969824

Diagnosis

Extraskeletal, intradural, non-metastatic Ewing's sarcoma. Case report.
Ottóffy G, Komáromy H
Ideggyogy Sz 2020 Jul 30;73(7-08):286-288. doi: 10.18071/isz.73.0268. PMID: 32750246
Primary spinal intradural extraskeletal Ewing sarcoma mimicking a giant nerve sheath tumor: case report and review of the literature.
Zhao M, Zhang B, Liang F, Zhang J
Int J Clin Exp Pathol 2014;7(12):9081-5. Epub 2014 Dec 1 PMID: 25674292Free PMC Article
A rare case of intradural extramedullary Ewing's sarcoma with skip metastasis in the spine.
Haresh KP, Chinikkatti SK, Prabhakar R, Rishi A, Rath GK, Sharma DN, Julka PK
Spinal Cord 2008 Aug;46(8):582-4. Epub 2008 Feb 12 doi: 10.1038/sc.2008.8. PMID: 18268515
Intradural, extramedullary spinal Ewing's sarcoma in childhood.
Uesaka T, Amano T, Inamura T, Ikezaki K, Inoha S, Takamatsu M, Iwaki T, Fukui M
J Clin Neurosci 2003 Jan;10(1):122-5. doi: 10.1016/s0967-5868(02)00279-5. PMID: 12464543
Neuroectodermal differentiation in "extraskeletal Ewing's sarcoma".
Kudo M
Acta Pathol Jpn 1989 Dec;39(12):795-802. PMID: 2560312

Prognosis

Primary spinal intradural extraskeletal Ewing sarcoma mimicking a giant nerve sheath tumor: case report and review of the literature.
Zhao M, Zhang B, Liang F, Zhang J
Int J Clin Exp Pathol 2014;7(12):9081-5. Epub 2014 Dec 1 PMID: 25674292Free PMC Article
Primary extraskeletal osteosarcoma in the pineal region. Case report.
Saesue P, Chankaew E, Chawalparit O, Na Ayudhya NS, Muangsomboon S, Sangruchi T
J Neurosurg 2004 Dec;101(6):1061-4. doi: 10.3171/jns.2004.101.6.1061. PMID: 15597771
Sarcoma metastatic to the brain: results of surgical treatment.
Bindal RK, Sawaya RE, Leavens ME, Taylor SH, Guinee VF
Neurosurgery 1994 Aug;35(2):185-90; discussion 190-1. doi: 10.1227/00006123-199408000-00002. PMID: 7969824

Clinical prediction guides

Extraskeletal, intradural, non-metastatic Ewing's sarcoma. Case report.
Ottóffy G, Komáromy H
Ideggyogy Sz 2020 Jul 30;73(7-08):286-288. doi: 10.18071/isz.73.0268. PMID: 32750246
Primary spinal intradural extraskeletal Ewing sarcoma mimicking a giant nerve sheath tumor: case report and review of the literature.
Zhao M, Zhang B, Liang F, Zhang J
Int J Clin Exp Pathol 2014;7(12):9081-5. Epub 2014 Dec 1 PMID: 25674292Free PMC Article
Reappraisal of mesenchymal chondrosarcoma: novel morphologic observations of the hyaline cartilage and endochondral ossification and beta-catenin, Sox9, and osteocalcin immunostaining of 22 cases.
Fanburg-Smith JC, Auerbach A, Marwaha JS, Wang Z, Rushing EJ
Hum Pathol 2010 May;41(5):653-62. doi: 10.1016/j.humpath.2009.11.006. PMID: 20138330
Primary extraskeletal osteosarcoma in the pineal region. Case report.
Saesue P, Chankaew E, Chawalparit O, Na Ayudhya NS, Muangsomboon S, Sangruchi T
J Neurosurg 2004 Dec;101(6):1061-4. doi: 10.3171/jns.2004.101.6.1061. PMID: 15597771
Sarcoma metastatic to the brain: results of surgical treatment.
Bindal RK, Sawaya RE, Leavens ME, Taylor SH, Guinee VF
Neurosurgery 1994 Aug;35(2):185-90; discussion 190-1. doi: 10.1227/00006123-199408000-00002. PMID: 7969824

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