Renal lymphangiectasia

MedGen UID:: 344661
•Concept ID:: C1856132
•: Finding

Synonyms:	Hygroma renale; Peripelvic lymphangiectasia; Renal lymphangiomatosis

HPO:	HP:6000073

Definition

A developmental anomaly of renal lymphatics that results from a failure of the lymphatics to make communication with the rest of the lymph trunks. The abnormal lymphatics thus dilate and form cystic spaces at the renal sinus and in the perinephric space. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVRenal lymphangiectasia

Congenital Systemic Disorder
- Abnormality of the genitourinary system
  - Abnormality of the urinary system
    - Abnormality of the upper urinary tract
      - Abnormality of the kidney
        Abnormal renal morphology
        Renal lymphangiectasia

Recent clinical studies

Etiology

Chronic renal insufficiency in a boy with cystic renal lymphangiectasia: morphological findings and long-term follow-up.

Ueda S, Yanagida H, Sugimoto K, Fujita S, Yagi K, Okada M, Takemura T
Clin Nephrol 2007 Dec;68(6):416-21. doi: 10.5414/cnp68416. PMID: 18184526

Cystic renal lymphangiectasia: a distinctive clinicopathologic entity in the pediatric age group.

Simonton SC, Saltzman DA, Brennom W, Pergament M, Drake G, Sinaiko A, Priest JR
Pediatr Pathol Lab Med 1997 Mar-Apr;17(2):293-301. PMID: 9086536

See all (2)

Diagnosis

Renal lymphangiectasia in pediatric population: case series and review of literature.

Alshanafey S, Alkhani A, Alkibsib A
Ann Saudi Med 2022 Mar-Apr;42(2):139-144. Epub 2022 Apr 7 doi: 10.5144/0256-4947.2022.139. PMID: 35380057 Free PMC Article

Renal lymphangiectasia.

Chen Z, Qi L, Tang Z, Hu Z, Fan B
Scand J Urol Nephrol 2009;43(5):428-30. doi: 10.3109/00365590902930857. PMID: 19921991

Renal lymphangiectasia.

Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

MRI findings of renal lymphangiectasia.

Kocaoglu M, Bulakbasi N, Ilica T, Somuncu I
J Magn Reson Imaging 2005 Nov;22(5):681-3. doi: 10.1002/jmri.20437. PMID: 16193474

Case 34: renal lymphangiectasia.

Ramseyer LT
Radiology 2001 May;219(2):442-4. doi: 10.1148/radiology.219.2.r01ma17442. PMID: 11323470

See all (22)

Therapy

Renal Lymphangiectasia in the Transplanted Kidney: Case Series and Literature Review.

Dawidek MT, Aquil S, Alogaili R, Gabril M, Moussa M, Sener A, Luke PP
Transplantation 2020 Jan;104(1):172-175. doi: 10.1097/TP.0000000000002745. PMID: 30964839

Role of CT scan in diagnosis of renal lymphangiectasia: our single-center experience.

Pandya VK, Sutariya HC, Gandhi SP, Khemchandani SI, Patel HV, Shah MK
Ren Fail 2017 Nov;39(1):533-539. doi: 10.1080/0886022X.2017.1337584. PMID: 28639460 Free PMC Article

Renal lymphangiectasia.

Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

See all (3)

Prognosis

Bilateral Renal Lymphangiectasia with No Significant Morbidity for Over 25 Years: A Case Report.

Alzahrani AM, Khamis AA, Barakat AE, Alotaibi K
Am J Case Rep 2021 Nov 8;22:e933934. doi: 10.12659/AJCR.933934. PMID: 34748529 Free PMC Article

Renal Lymphangiectasia in a Pediatric Patient.

Desai SB, Sun RC, Johnson BL, Rialon KL, Iacobas I, Kukreja KU, Schady DA, Phung T, Sanvitha S, Naik-Mathuria BJ
Lymphat Res Biol 2020 Dec;18(6):572-578. Epub 2020 Jun 24 doi: 10.1089/lrb.2020.0004. PMID: 32589505

Chronic renal insufficiency in a boy with cystic renal lymphangiectasia: morphological findings and long-term follow-up.

Ueda S, Yanagida H, Sugimoto K, Fujita S, Yagi K, Okada M, Takemura T
Clin Nephrol 2007 Dec;68(6):416-21. doi: 10.5414/cnp68416. PMID: 18184526

Renal lymphangiectasia.

Ashraf K, Raza SS, Ashraf O, Memon W, Memon A, Zubairi TA
Br J Radiol 2007 Jun;80(954):e117-8. doi: 10.1259/bjr/16931054. PMID: 17684071

See all (4)