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Biliary System Disorder

MedGen UID:
476757
•Concept ID:
C3275124
•
Disease or Syndrome
Synonyms: Biliary Disease; Biliary Disorder

Definition

A non-neoplastic or neoplastic disorder that affects the intrahepatic or extrahepatic bile ducts or the gallbladder. Representative examples of non-neoplastic disorders include cholangitis and cholecystitis. Representative examples of neoplastic disorders include extrahepatic bile duct adenoma, intrahepatic and extrahepatic cholangiocarcinoma, and gallbladder carcinoma. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBiliary System Disorder

Professional guidelines

PubMed

Diagnosis and management of choledochal cysts.
Brown ZJ, Baghdadi A, Kamel I, Labiner HE, Hewitt DB, Pawlik TM
HPB (Oxford) 2023 Jan;25(1):14-25. Epub 2022 Oct 5 doi: 10.1016/j.hpb.2022.09.010. PMID: 36257874
Tokyo Guidelines 2018: diagnostic criteria and severity grading of acute cholecystitis (with videos).
Yokoe M, Hata J, Takada T, Strasberg SM, Asbun HJ, Wakabayashi G, Kozaka K, Endo I, Deziel DJ, Miura F, Okamoto K, Hwang TL, Huang WS, Ker CG, Chen MF, Han HS, Yoon YS, Choi IS, Yoon DS, Noguchi Y, Shikata S, Ukai T, Higuchi R, Gabata T, Mori Y, Iwashita Y, Hibi T, Jagannath P, Jonas E, Liau KH, Dervenis C, Gouma DJ, Cherqui D, Belli G, Garden OJ, Giménez ME, de Santibañes E, Suzuki K, Umezawa A, Supe AN, Pitt HA, Singh H, Chan ACW, Lau WY, Teoh AYB, Honda G, Sugioka A, Asai K, Gomi H, Itoi T, Kiriyama S, Yoshida M, Mayumi T, Matsumura N, Tokumura H, Kitano S, Hirata K, Inui K, Sumiyama Y, Yamamoto M
J Hepatobiliary Pancreat Sci 2018 Jan;25(1):41-54. Epub 2018 Jan 9 doi: 10.1002/jhbp.515. PMID: 29032636
IAP/APA evidence-based guidelines for the management of acute pancreatitis.
Working Group IAP/APA Acute Pancreatitis Guidelines
Pancreatology 2013 Jul-Aug;13(4 Suppl 2):e1-15. doi: 10.1016/j.pan.2013.07.063. PMID: 24054878

Recent clinical studies

Etiology

Cholangiocarcinoma.
Brindley PJ, Bachini M, Ilyas SI, Khan SA, Loukas A, Sirica AE, Teh BT, Wongkham S, Gores GJ
Nat Rev Dis Primers 2021 Sep 9;7(1):65. doi: 10.1038/s41572-021-00300-2. PMID: 34504109Free PMC Article
International consensus statements for endoscopic management of distal biliary stricture.
Nakai Y, Isayama H, Wang HP, Rerknimitr R, Khor C, Yasuda I, Kogure H, Moon JH, Lau J, Lakhtakia S, Ratanachu-Ek T, Seo DW, Lee DK, Makmun D, Dy F, Liao WC, Draganov PV, Almadi M, Irisawa A, Katanuma A, Kitano M, Ryozawa S, Fujisawa T, Wallace MB, Itoi T, Devereaux B
J Gastroenterol Hepatol 2020 Jun;35(6):967-979. Epub 2020 Jan 10 doi: 10.1111/jgh.14955. PMID: 31802537Free PMC Article
Acute cholangitis: Diagnosis and management.
Sokal A, Sauvanet A, Fantin B, de Lastours V
J Visc Surg 2019 Dec;156(6):515-525. Epub 2019 Jun 24 doi: 10.1016/j.jviscsurg.2019.05.007. PMID: 31248783
Gallstones.
Lammert F, Gurusamy K, Ko CW, Miquel JF, Méndez-Sánchez N, Portincasa P, van Erpecum KJ, van Laarhoven CJ, Wang DQ
Nat Rev Dis Primers 2016 Apr 28;2:16024. doi: 10.1038/nrdp.2016.24. PMID: 27121416
Biliary cystic disease.
Levy AD, Rohrmann CA Jr
Curr Probl Diagn Radiol 2003 Nov-Dec;32(6):233-63. doi: 10.1016/j.cpradiol.2003.08.002. PMID: 14647122

Diagnosis

Acute cholangitis: Diagnosis and management.
Sokal A, Sauvanet A, Fantin B, de Lastours V
J Visc Surg 2019 Dec;156(6):515-525. Epub 2019 Jun 24 doi: 10.1016/j.jviscsurg.2019.05.007. PMID: 31248783
Diagnosis and management of biliary injuries.
Rose JB, Hawkins WG
Curr Probl Surg 2017 Aug;54(8):406-435. Epub 2017 Jul 24 doi: 10.1067/j.cpsurg.2017.06.001. PMID: 28987473
Gallstones.
Lammert F, Gurusamy K, Ko CW, Miquel JF, Méndez-Sánchez N, Portincasa P, van Erpecum KJ, van Laarhoven CJ, Wang DQ
Nat Rev Dis Primers 2016 Apr 28;2:16024. doi: 10.1038/nrdp.2016.24. PMID: 27121416
Nanoparticle-liver interactions: Cellular uptake and hepatobiliary elimination.
Zhang YN, Poon W, Tavares AJ, McGilvray ID, Chan WCW
J Control Release 2016 Oct 28;240:332-348. Epub 2016 Jan 13 doi: 10.1016/j.jconrel.2016.01.020. PMID: 26774224
Biliary cystic disease.
Levy AD, Rohrmann CA Jr
Curr Probl Diagn Radiol 2003 Nov-Dec;32(6):233-63. doi: 10.1016/j.cpradiol.2003.08.002. PMID: 14647122

Therapy

Integrating cytotoxic, targeted and immune therapies for cholangiocarcinoma.
Merters J, Lamarca A
J Hepatol 2023 Mar;78(3):652-657. Epub 2022 Nov 15 doi: 10.1016/j.jhep.2022.11.005. PMID: 36400328
The Landmark Series: Hilar Cholangiocarcinoma.
Soares KC, Jarnagin WR
Ann Surg Oncol 2021 Aug;28(8):4158-4170. Epub 2021 Apr 7 doi: 10.1245/s10434-021-09871-6. PMID: 33829358Free PMC Article
Acute cholangitis: Diagnosis and management.
Sokal A, Sauvanet A, Fantin B, de Lastours V
J Visc Surg 2019 Dec;156(6):515-525. Epub 2019 Jun 24 doi: 10.1016/j.jviscsurg.2019.05.007. PMID: 31248783
Multimodality Management of Localized Biliary Cancer.
Ashai N, Prasad P, Rajdev L
Curr Treat Options Oncol 2019 May 29;20(7):58. doi: 10.1007/s11864-019-0655-0. PMID: 31144050
Diagnosis and management of biliary injuries.
Rose JB, Hawkins WG
Curr Probl Surg 2017 Aug;54(8):406-435. Epub 2017 Jul 24 doi: 10.1067/j.cpsurg.2017.06.001. PMID: 28987473

Prognosis

Acute cholangitis: Diagnosis and management.
Sokal A, Sauvanet A, Fantin B, de Lastours V
J Visc Surg 2019 Dec;156(6):515-525. Epub 2019 Jun 24 doi: 10.1016/j.jviscsurg.2019.05.007. PMID: 31248783
Diagnosis and management of biliary injuries.
Rose JB, Hawkins WG
Curr Probl Surg 2017 Aug;54(8):406-435. Epub 2017 Jul 24 doi: 10.1067/j.cpsurg.2017.06.001. PMID: 28987473
Biliary dyskinesia.
Vassiliou MC, Laycock WS
Surg Clin North Am 2008 Dec;88(6):1253-72, viii-ix. doi: 10.1016/j.suc.2008.07.004. PMID: 18992594
Cholangiocarcinoma.
Blechacz BR, Gores GJ
Clin Liver Dis 2008 Feb;12(1):131-50, ix. doi: 10.1016/j.cld.2007.11.003. PMID: 18242501
AIDS-Related biliary tract disease.
Cello JP
Gastrointest Endosc Clin N Am 1998 Oct;8(4):963. PMID: 9730942

Clinical prediction guides

Acquisition of epithelial plasticity in human chronic liver disease.
Gribben C, Galanakis V, Calderwood A, Williams EC, Chazarra-Gil R, Larraz M, Frau C, Puengel T, Guillot A, Rouhani FJ, Mahbubani K, Godfrey E, Davies SE, Athanasiadis E, Saeb-Parsy K, Tacke F, Allison M, Mohorianu I, Vallier L
Nature 2024 Jun;630(8015):166-173. Epub 2024 May 22 doi: 10.1038/s41586-024-07465-2. PMID: 38778114Free PMC Article
Acute pancreatitis: A review of diagnosis, severity prediction and prognosis assessment from imaging technology, scoring system and artificial intelligence.
Hu JX, Zhao CF, Wang SL, Tu XY, Huang WB, Chen JN, Xie Y, Chen CR
World J Gastroenterol 2023 Oct 7;29(37):5268-5291. doi: 10.3748/wjg.v29.i37.5268. PMID: 37899784Free PMC Article
BRCAness in biliary tract cancer: a new prognostic and predictive biomarker?
Hachem S, Kassis Y, Hachem MC, Zouein J, Gharios J, Kourie HR
Biomark Med 2023 Jan;17(1):51-57. Epub 2023 Mar 30 doi: 10.2217/bmm-2022-0664. PMID: 36994675
Ultrasonographic patterns, clinical findings, and prognostic variables in dogs from Asia with gallbladder mucocele.
Jaffey JA, Kreisler R, Shumway K, Lee YJ, Lin CH, Durocher-Babek LL, Seo KW, Choi H, Nakashima K, Harada H, Kanemoto H, Lin LS
J Vet Intern Med 2022 Mar;36(2):565-575. Epub 2022 Feb 15 doi: 10.1111/jvim.16384. PMID: 35170083Free PMC Article
Acute cholangitis: Diagnosis and management.
Sokal A, Sauvanet A, Fantin B, de Lastours V
J Visc Surg 2019 Dec;156(6):515-525. Epub 2019 Jun 24 doi: 10.1016/j.jviscsurg.2019.05.007. PMID: 31248783

Recent systematic reviews

Methylphenidate for children and adolescents with attention deficit hyperactivity disorder (ADHD).
Storebø OJ, Storm MRO, Pereira Ribeiro J, Skoog M, Groth C, Callesen HE, Schaug JP, Darling Rasmussen P, Huus CL, Zwi M, Kirubakaran R, Simonsen E, Gluud C
Cochrane Database Syst Rev 2023 Mar 27;3(3):CD009885. doi: 10.1002/14651858.CD009885.pub3. PMID: 36971690Free PMC Article
Management of symptomatic cholelithiasis: a systematic review.
Shenoy R, Kirkland P, Hadaya JE, Tranfield MW, DeVirgilio M, Russell MM, Maggard-Gibbons M
Syst Rev 2022 Dec 12;11(1):267. doi: 10.1186/s13643-022-02135-8. PMID: 36510302Free PMC Article
Extrapelvic Endometriosis: A Systematic Review.
Andres MP, Arcoverde FVL, Souza CCC, Fernandes LFC, Abrão MS, Kho RM
J Minim Invasive Gynecol 2020 Feb;27(2):373-389. Epub 2019 Oct 13 doi: 10.1016/j.jmig.2019.10.004. PMID: 31618674
Long-Term Impact of Iatrogenic Bile Duct Injury.
Schreuder AM, Busch OR, Besselink MG, Ignatavicius P, Gulbinas A, Barauskas G, Gouma DJ, van Gulik TM
Dig Surg 2020;37(1):10-21. Epub 2019 Jan 17 doi: 10.1159/000496432. PMID: 30654363Free PMC Article
Acute cholecystitis.
Halpin V
BMJ Clin Evid 2014 Aug 20;2014 PMID: 25144428Free PMC Article

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