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Skin Myxofibrosarcoma

MedGen UID:
699196
Concept ID:
C1275975
Neoplastic Process
Synonyms: Dermal Myxofibrosarcoma; Myxofibrosarcoma of skin; Myxoid malignant fibrous histiocytoma of skin
SNOMED CT: Myxofibrosarcoma of skin (400175006); Myxoid malignant fibrous histiocytoma of skin (400175006)

Definition

Myxofibrosarcoma that arises from the dermis. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSkin Myxofibrosarcoma

Professional guidelines

PubMed

Borgognoni L, Pescitelli L, Gerlini G, Brandani P, Gelli R, Giannotti V, Bellucci F, Sestini S
Anticancer Res 2020 Nov;40(11):6485-6492. doi: 10.21873/anticanres.14670. PMID: 33109587
Pretell-Mazzini J, Barton MD Jr, Conway SA, Temple HT
J Bone Joint Surg Am 2015 Apr 1;97(7):597-603. doi: 10.2106/JBJS.N.00649. PMID: 25834085
Mansoor A, White CR Jr
Am J Dermatopathol 2003 Aug;25(4):281-6. doi: 10.1097/00000372-200308000-00001. PMID: 12876484

Recent clinical studies

Etiology

Villy MC, Le Ven A, Le Mentec M, Masliah-Planchon J, Houy A, Bièche I, Vacher S, Vincent-Salomon A, Dubois d'Enghien C, Schwartz M, Piperno-Neumann S, Matet A, Malaise D, Bubien V, Lortholary A, Ait Omar A, Cavaillé M, Stoppa-Lyonnet D, Cassoux N, Stern MH, Rodrigues M, Golmard L, Colas C
J Natl Cancer Inst 2024 Apr 5;116(4):580-587. doi: 10.1093/jnci/djad248. PMID: 38060262
Haseli S, Mansoori B, Christensen D, Abadi A, Pooyan A, Shomal Zadeh F, Mau B, Khalili N, Murphey M, Chalian M
Radiographics 2023 Aug;43(8):e230005. doi: 10.1148/rg.230005. PMID: 37440448
Liu CK, Williamson JE 3rd, Milman T, Lally SE, Shields CL
Ophthalmic Plast Reconstr Surg 2022 Nov-Dec 01;38(6):e180-e183. Epub 2022 Jul 4 doi: 10.1097/IOP.0000000000002236. PMID: 35793663
Singh A, Brar RK, Dey B, Nigam J, Deshpande A
J Cutan Pathol 2019 May;46(5):376-379. Epub 2019 Mar 22 doi: 10.1111/cup.13432. PMID: 30681740
Sakamoto A, Shiba E, Hisaoka M
Skeletal Radiol 2014 Oct;43(10):1487-90. Epub 2014 Jun 10 doi: 10.1007/s00256-014-1914-6. PMID: 24910124

Diagnosis

DeBiasio C, Glassman SJ
J Cutan Med Surg 2024 May-Jun;28(3):314. Epub 2024 Feb 2 doi: 10.1177/12034754241229352. PMID: 38303656
Cammareri C, Beltzung F, Michal M, Vanhersecke L, Coindre JM, Velasco V, Le Loarer F, Vergier B, Perret R
Virchows Arch 2023 Aug;483(2):145-156. Epub 2023 Jul 21 doi: 10.1007/s00428-023-03606-6. PMID: 37477762
Yamada Y, Ichiki T, Susuki Y, Yamada-Nozaki Y, Tateishi Y, Furue M, Oda Y
J Clin Pathol 2023 Aug;76(8):536-540. Epub 2022 Mar 22 doi: 10.1136/jclinpath-2022-208158. PMID: 35318257
Liu CK, Williamson JE 3rd, Milman T, Lally SE, Shields CL
Ophthalmic Plast Reconstr Surg 2022 Nov-Dec 01;38(6):e180-e183. Epub 2022 Jul 4 doi: 10.1097/IOP.0000000000002236. PMID: 35793663
de Castro BA, Piancastelli AC, Meyer RL, Piancastelli PM, Ribeiro CA, Miranda RM
An Bras Dermatol 2016 Jan-Feb;91(1):97-9. doi: 10.1590/abd1806-4841.20163922. PMID: 26982788Free PMC Article

Therapy

Wang D, Harris J, Kraybill WG, Eisenberg B, Kirsch DG, Ettinger DS, Kane JM 3rd, Barry PN, Naghavi A, Freeman CR, Chen YL, Hitchcock YJ, Bedi M, Salerno KE, Severin D, Godette KD, Larrier NA, Curran WJ Jr, Torres-Saavedra PA, Lucas DR
JAMA Oncol 2023 May 1;9(5):646-655. doi: 10.1001/jamaoncol.2023.0042. PMID: 36995690Free PMC Article
Uwa N, Terada T, Mohri T, Tsukamoto Y, Futani H, Demizu Y, Okimoto T, Sakagami M
Auris Nasus Larynx 2017 Aug;44(4):484-488. Epub 2016 Aug 11 doi: 10.1016/j.anl.2016.07.016. PMID: 27523716
Karanian M, Pérot G, Coindre JM, Chibon F, Pedeutour F, Neuville A
Mod Pathol 2015 Feb;28(2):230-7. Epub 2014 Aug 1 doi: 10.1038/modpathol.2014.97. PMID: 25081750
Smith SC, Poznanski AA, Fullen DR, Ma L, McHugh JB, Lucas DR, Patel RM
J Cutan Pathol 2013 Jul;40(7):639-45. Epub 2013 Apr 19 doi: 10.1111/cup.12158. PMID: 23600956
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051

Prognosis

Freeland J, Muñoz M, O'Donnell E 3rd, Langerman J, Darrow M, Bergonio J, Suarez-Navarro J, Thorpe S, Canter R, Randall RL, Plath K, Carraway KL 3rd, Witte ON, Graeber TG, Carr-Ascher JR
Clin Cancer Res 2024 Nov 1;30(21):4957-4973. doi: 10.1158/1078-0432.CCR-24-1238. PMID: 39177582Free PMC Article
Liu CK, Williamson JE 3rd, Milman T, Lally SE, Shields CL
Ophthalmic Plast Reconstr Surg 2022 Nov-Dec 01;38(6):e180-e183. Epub 2022 Jul 4 doi: 10.1097/IOP.0000000000002236. PMID: 35793663
Sakamoto A, Shiba E, Hisaoka M
Skeletal Radiol 2014 Oct;43(10):1487-90. Epub 2014 Jun 10 doi: 10.1007/s00256-014-1914-6. PMID: 24910124
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
Mentzel T
Clin Dermatol 2011 Jan-Feb;29(1):80-90. doi: 10.1016/j.clindermatol.2010.07.011. PMID: 21146736

Clinical prediction guides

Nakata E, Fujiwara T, Kunisada T, Nakahara R, Katayama H, Itano T, Ozaki T
J Orthop Surg Res 2023 Aug 14;18(1):599. doi: 10.1186/s13018-023-04088-7. PMID: 37580775Free PMC Article
Haseli S, Mansoori B, Christensen D, Abadi A, Pooyan A, Shomal Zadeh F, Mau B, Khalili N, Murphey M, Chalian M
Radiographics 2023 Aug;43(8):e230005. doi: 10.1148/rg.230005. PMID: 37440448
Musser E, Smolle M, Friesenbichler J, Leithner A, Bergovec M
Orthop Traumatol Surg Res 2019 Oct;105(6):1211-1213. Epub 2019 Jun 14 doi: 10.1016/j.otsr.2019.04.013. PMID: 31208933
Rupp NJ, Rechsteiner M, Freiberger SN, Lenggenhager D, Urosevic M, Burger IA, Rushing EJ, Mihic-Probst D
Virchows Arch 2018 Oct;473(4):517-521. Epub 2018 May 21 doi: 10.1007/s00428-018-2376-3. PMID: 29785541
Brenn T
Adv Anat Pathol 2014 Mar;21(2):108-30. doi: 10.1097/PAP.0000000000000009. PMID: 24508694

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