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Meningeal sarcoma

MedGen UID:
90148
Concept ID:
C0302327
Neoplastic Process
Synonyms: meningeal cluster sarcoma; Meningeal Sarcoma; meningeal sarcoma; Meninges Sarcoma; meninges sarcoma; Meningothelial sarcoma; sarcoma of meningeal cluster; Sarcoma of Meninges; sarcoma of meninges; Sarcoma of the Meninges; sarcoma of the meninges
SNOMED CT: Meningeal sarcoma (78303004); Meningothelial sarcoma (78303004)
 
Monarch Initiative: MONDO:0004308

Definition

A rare sarcoma arising from the meninges. [from NCI]

Professional guidelines

PubMed

Esmaeilzadeh M, Uksul N, Hong B, von Kaisenberg C, Scheinichen D, Lang JM, Hermann EJ, Hillemanns P, Krauss JK
Clin Neurol Neurosurg 2020 Aug;195:105905. Epub 2020 May 12 doi: 10.1016/j.clineuro.2020.105905. PMID: 32428795

Recent clinical studies

Etiology

Vrána D, Kalita O, Hrabálek L, Matzenauer M, Bartoušková M, Rušarová N, Tučková L, Sedláčková L
Klin Onkol 2019 Spring;32(3):214-219. doi: 10.14735/amko2019214. PMID: 31216855
Bilginer B, Türk CC, Narin F, Hazer B, Hanalioglu S, Oguz KK, Soylemezoglu F, Akalan N
Childs Nerv Syst 2015 Jun;31(6):893-9. Epub 2015 Apr 2 doi: 10.1007/s00381-015-2689-3. PMID: 25831997
Minniti G, Traish D, Ashley S, Gonsalves A, Brada M
J Clin Endocrinol Metab 2005 Feb;90(2):800-4. Epub 2004 Nov 23 doi: 10.1210/jc.2004-1152. PMID: 15562021
Hope JK, Armstrong DA, Babyn PS, Humphreys RR, Harwood-Nash DC, Chuang SH, Marks PV
AJNR Am J Neuroradiol 1992 Sep-Oct;13(5):1353-64. PMID: 1414828Free PMC Article
Raney RB Jr, Tefft M, Newton WA, Ragab AH, Lawrence W Jr, Gehan EA, Maurer HM
Cancer 1987 Jan 1;59(1):147-55. doi: 10.1002/1097-0142(19870101)59:1<147::aid-cncr2820590129>3.0.co;2-8. PMID: 3791141

Diagnosis

Esmaeilzadeh M, Uksul N, Hong B, von Kaisenberg C, Scheinichen D, Lang JM, Hermann EJ, Hillemanns P, Krauss JK
Clin Neurol Neurosurg 2020 Aug;195:105905. Epub 2020 May 12 doi: 10.1016/j.clineuro.2020.105905. PMID: 32428795
Bernal García LM, Cabezudo Artero JM, Royano Sánchez M, Marcelo Zamorano MB, López Macías M
Childs Nerv Syst 2015 Jul;31(7):1177-80. Epub 2015 Apr 12 doi: 10.1007/s00381-015-2703-9. PMID: 25863951
Barbagallo GM, Lanzafame S, Nicol eG, Platania N, Albanese V
J Neurosurg 2002 Mar;96(2 Suppl):230-5. doi: 10.3171/spi.2002.96.2.0230. PMID: 12450287
Büttner A, Pfluger T, Weis S
J Neurooncol 2001 Apr;52(2):181-8. doi: 10.1023/a:1010662818560. PMID: 11508818
Raney RB Jr, Tefft M, Newton WA, Ragab AH, Lawrence W Jr, Gehan EA, Maurer HM
Cancer 1987 Jan 1;59(1):147-55. doi: 10.1002/1097-0142(19870101)59:1<147::aid-cncr2820590129>3.0.co;2-8. PMID: 3791141

Therapy

Vrána D, Kalita O, Hrabálek L, Matzenauer M, Bartoušková M, Rušarová N, Tučková L, Sedláčková L
Klin Onkol 2019 Spring;32(3):214-219. doi: 10.14735/amko2019214. PMID: 31216855
Bilginer B, Türk CC, Narin F, Hazer B, Hanalioglu S, Oguz KK, Soylemezoglu F, Akalan N
Childs Nerv Syst 2015 Jun;31(6):893-9. Epub 2015 Apr 2 doi: 10.1007/s00381-015-2689-3. PMID: 25831997
Hoff AO, Vassilopoulou-Sellin R
Cancer 1998 Apr 15;82(8):1585-92. PMID: 9554538
Brada M, Ford D, Ashley S, Bliss JM, Crowley S, Mason M, Rajan B, Traish D
BMJ 1992 May 23;304(6838):1343-6. doi: 10.1136/bmj.304.6838.1343. PMID: 1611331Free PMC Article
Raney RB Jr, Tefft M, Newton WA, Ragab AH, Lawrence W Jr, Gehan EA, Maurer HM
Cancer 1987 Jan 1;59(1):147-55. doi: 10.1002/1097-0142(19870101)59:1<147::aid-cncr2820590129>3.0.co;2-8. PMID: 3791141

Prognosis

Esmaeilzadeh M, Uksul N, Hong B, von Kaisenberg C, Scheinichen D, Lang JM, Hermann EJ, Hillemanns P, Krauss JK
Clin Neurol Neurosurg 2020 Aug;195:105905. Epub 2020 May 12 doi: 10.1016/j.clineuro.2020.105905. PMID: 32428795
Vrána D, Kalita O, Hrabálek L, Matzenauer M, Bartoušková M, Rušarová N, Tučková L, Sedláčková L
Klin Onkol 2019 Spring;32(3):214-219. doi: 10.14735/amko2019214. PMID: 31216855
Bernal García LM, Cabezudo Artero JM, Royano Sánchez M, Marcelo Zamorano MB, López Macías M
Childs Nerv Syst 2015 Jul;31(7):1177-80. Epub 2015 Apr 12 doi: 10.1007/s00381-015-2703-9. PMID: 25863951
Büttner A, Pfluger T, Weis S
J Neurooncol 2001 Apr;52(2):181-8. doi: 10.1023/a:1010662818560. PMID: 11508818
Hope JK, Armstrong DA, Babyn PS, Humphreys RR, Harwood-Nash DC, Chuang SH, Marks PV
AJNR Am J Neuroradiol 1992 Sep-Oct;13(5):1353-64. PMID: 1414828Free PMC Article

Clinical prediction guides

Bernal García LM, Cabezudo Artero JM, Royano Sánchez M, Marcelo Zamorano MB, López Macías M
Childs Nerv Syst 2015 Jul;31(7):1177-80. Epub 2015 Apr 12 doi: 10.1007/s00381-015-2703-9. PMID: 25863951
Sugita Y, Shigemori M, Harada H, Wada Y, Hayashi I, Morimastu M, Okamoto Y, Kajiwara K
Am J Surg Pathol 2000 Sep;24(9):1273-8. doi: 10.1097/00000478-200009000-00011. PMID: 10976702
Jones PD, Henry RL, Gibson PG, Hankin R, Carty K
Pediatr Pulmonol 1998 Jul;26(1):74-7. doi: 10.1002/(sici)1099-0496(199807)26:1<74::aid-ppul11>3.0.co;2-5. PMID: 9710282
Hoff AO, Vassilopoulou-Sellin R
Cancer 1998 Apr 15;82(8):1585-92. PMID: 9554538
Henson JW, Cordon-Cardo C, Posner JB
J Neurooncol 1992 Sep;14(1):37-43. doi: 10.1007/BF00170943. PMID: 1361524

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