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Enterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor

MedGen UID:
91057
•Concept ID:
C0345933
•
Neoplastic Process
Synonyms: carcinoid neoplasm of pancreas; carcinoid neoplasm of the pancreas; Carcinoid tumor of pancreas; carcinoid tumor of pancreas; carcinoid tumor of the pancreas; carcinoid tumour of pancreas; carcinoid tumour of the pancreas; EC Cell, Serotonin Producing Pancreatic NET; EC cell, serotonin producing pancreatic NET; EC Cell, Serotonin Producing Pancreatic Neuroendocrine Tumor; EC cell, serotonin producing pancreatic neuroendocrine tumor; EC cell, serotonin producing pancreatic neuroendocrine tumour; Enterochromaffin Cell Serotonin-Producing Pancreatic Neuroendocrine Tumor; enterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor; pancreatic carcinoid tumor; pancreatic carcinoid tumour; Pancreatic Serotonin Producing Neoplasm; pancreatic serotonin producing neoplasm; Pancreatic Serotonin Producing Tumor; pancreatic serotonin producing tumor; pancreatic serotonin producing tumour; Pancreatic Serotonin-Producing Neuroendocrine Tumor; serotonin-producing neuroendocrine tumor of pancreas; Serotonin-producing neuroendocrine tumor of pancreas; serotonin-producing neuroendocrine tumour of pancreas; serotonin-producing pancreatic NET; Serotonin-producing pancreatic NET; Serotonin-Producing Pancreatic Neuroendocrine Tumor; Serotonin-producing pancreatic neuroendocrine tumor; serotonin-producing pancreatic neuroendocrine tumor; serotonin-producing pancreatic neuroendocrine tumour; Serotonin-producing PNET; serotonin-producing PNET; Serotonin-Producing Tumor of Pancreas; serotonin-producing tumor of pancreas; Serotonin-Producing Tumor of the Pancreas; serotonin-producing tumor of the pancreas; serotonin-producing tumour of pancreas; serotonin-producing tumour of the pancreas
SNOMED CT: Carcinoid tumor of pancreas (254613007)
 
Monarch Initiative: MONDO:0024504
Orphanet: ORPHA506090

Definition

A rare functioning neuroendocrine tumor of pancreas characterized by a typically well-differentiated neoplasm composed of cells expressing serotonin. Patients may present with atypical carcinoid syndrome with abdominal pain, diarrhea, weight loss, and/or flushing. Carcinoid syndrome is usually present only when there are liver metastases. The tumors tend to be larger than non-functioning tumors and are associated with a poorer prognosis because they are almost always metastatic. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEnterochromaffin cell serotonin-producing pancreatic neuroendocrine tumor

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