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Ariboflavinosis

MedGen UID:
20573
Concept ID:
C0035528
Disease or Syndrome
Synonyms: Decreased circulating vitamin B2 concentration; Riboflavin deficiency
SNOMED CT: Riboflavine deficiency (20307000); Ariboflavinosis (20307000); Vitamin B2 deficiency (20307000); Riboflavin deficiency (20307000)
 
Gene (location): SLC52A1 (17p13.2)
 
HPO: HP:0100504
Monarch Initiative: MONDO:0004573
OMIM®: 615026

Definition

The concentration of vitamin B2 in the blood circulation is below the lower limit of normal. [from HPO]

Clinical features

From HPO
Dicarboxylic aciduria
MedGen UID:
343550
Concept ID:
C1856432
Finding
An increased concentration of dicarboxylic acid in the urine.
Poor suck
MedGen UID:
324693
Concept ID:
C1837142
Finding
An inadequate sucking reflex, resulting in the difficult of newborns to be breast-fed.
Lethargy
MedGen UID:
7310
Concept ID:
C0023380
Sign or Symptom
A state of fatigue, either physical or mental slowness and sluggishness, with difficulties in initiating or performing simple tasks. Distinguished from apathy which implies indifference and a lack of desire or interest in the task. A person with lethargy may have the desire, but not the energy to engage in personal or socially relevant tasks.
Hypotonia
MedGen UID:
10133
Concept ID:
C0026827
Finding
Hypotonia is an abnormally low muscle tone (the amount of tension or resistance to movement in a muscle). Even when relaxed, muscles have a continuous and passive partial contraction which provides some resistance to passive stretching. Hypotonia thus manifests as diminished resistance to passive stretching. Hypotonia is not the same as muscle weakness, although the two conditions can co-exist.
Lactic acidosis
MedGen UID:
1717
Concept ID:
C0001125
Disease or Syndrome
An abnormal buildup of lactic acid in the body, leading to acidification of the blood and other bodily fluids.
Hypoglycemia
MedGen UID:
6979
Concept ID:
C0020615
Disease or Syndrome
A decreased concentration of glucose in the blood.
Hypothermia
MedGen UID:
5720
Concept ID:
C0020672
Finding
Reduced body temperature due to failed thermoregulation.
Ariboflavinosis
MedGen UID:
20573
Concept ID:
C0035528
Disease or Syndrome
The concentration of vitamin B2 in the blood circulation is below the lower limit of normal.
Metabolic acidosis
MedGen UID:
65117
Concept ID:
C0220981
Pathologic Function
Metabolic acidosis (MA) is characterized by a fall in blood pH due to a reduction of serum bicarbonate concentration. This can occur as a result of either the accumulation of acids (high anion gap MA) or the loss of bicarbonate from the gastrointestinal tract or the kidney (hyperchloremic MA). By definition, MA is not due to a respirary cause.
Elevated circulating acylcarnitine concentration
MedGen UID:
892855
Concept ID:
C4073171
Finding
Concentration of acylcarnitine in the blood circulation above the upper limit of normal.

Conditions with this feature

Ariboflavinosis
MedGen UID:
20573
Concept ID:
C0035528
Disease or Syndrome
The concentration of vitamin B2 in the blood circulation is below the lower limit of normal.

Professional guidelines

PubMed

McAuley E, McNulty H, Hughes C, Strain JJ, Ward M
Proc Nutr Soc 2016 Aug;75(3):405-14. Epub 2016 May 12 doi: 10.1017/S0029665116000197. PMID: 27170501
Reilly R, McNulty H, Pentieva K, Strain JJ, Ward M
Proc Nutr Soc 2014 Feb;73(1):47-56. Epub 2013 Oct 17 doi: 10.1017/S0029665113003613. PMID: 24131523
Horvath R
J Inherit Metab Dis 2012 Jul;35(4):679-87. Epub 2012 Jan 10 doi: 10.1007/s10545-011-9434-1. PMID: 22231380

Recent clinical studies

Etiology

Roughead ZK, McCormick DB
Eur J Clin Nutr 1991 Jun;45(6):299-307. PMID: 1915203
Thurnham DI, Rathakette P, Hambidge KM, Munoz N, Crespi M
Hum Nutr Clin Nutr 1982;36(5):337-49. PMID: 7174357

Diagnosis

Thurnham DI
Ann Trop Med Parasitol 1972 Dec;66(4):505-8. doi: 10.1080/00034983.1972.11686853. PMID: 4656452

Therapy

Mushtaq S, Su H, Hill MH, Powers HJ
Am J Clin Nutr 2009 Nov;90(5):1151-9. Epub 2009 Sep 9 doi: 10.3945/ajcn.2009.28338. PMID: 19740970
Roughead ZK, McCormick DB
Eur J Clin Nutr 1991 Jun;45(6):299-307. PMID: 1915203
Ajayi OA, James OA
Am J Clin Nutr 1984 May;39(5):787-91. doi: 10.1093/ajcn/39.5.787. PMID: 6711480
Thurnham DI
Ann Trop Med Parasitol 1972 Dec;66(4):505-8. doi: 10.1080/00034983.1972.11686853. PMID: 4656452
Ascher KW
Eye Ear Nose Throat Mon 1969 Dec;48(12):685-8. PMID: 5353175

Clinical prediction guides

GERBASI M
Arch Pediatr (N Y) 1960 Apr;77:157-64. PMID: 13704534

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