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Immunodeficiency, X-linked, with hyper-IgM

MedGen UID:
942082
Concept ID:
CN259046
Disease or Syndrome

Professional guidelines

PubMed

França TT, Barreiros LA, Al-Ramadi BK, Ochs HD, Cabral-Marques O, Condino-Neto A
Expert Rev Clin Immunol 2019 May;15(5):529-540. Epub 2019 Feb 18 doi: 10.1080/1744666X.2019.1573674. PMID: 30681380
Yazdani R, Fekrvand S, Shahkarami S, Azizi G, Moazzami B, Abolhassani H, Aghamohammadi A
Clin Immunol 2019 Jan;198:19-30. Epub 2018 Nov 13 doi: 10.1016/j.clim.2018.11.007. PMID: 30439505
Kawai T, Nishikomori R, Heike T
Allergol Int 2012 Jun;61(2):207-17. doi: 10.2332/allergolint.12-RAI-0446. PMID: 22635013

Recent clinical studies

Etiology

Kuo CY
Curr Opin Allergy Clin Immunol 2018 Dec;18(6):453-458. doi: 10.1097/ACI.0000000000000483. PMID: 30299399
Kanegane H, Hoshino A, Okano T, Yasumi T, Wada T, Takada H, Okada S, Yamashita M, Yeh TW, Nishikomori R, Takagi M, Imai K, Ochs HD, Morio T
Allergol Int 2018 Jan;67(1):43-54. Epub 2017 Jul 3 doi: 10.1016/j.alit.2017.06.003. PMID: 28684198
Qamar N, Fuleihan RL
Clin Rev Allergy Immunol 2014 Apr;46(2):120-30. doi: 10.1007/s12016-013-8378-7. PMID: 23797640
An Y, Xiao J, Jiang L, Yang X, Yu J, Zhao X
Scand J Immunol 2010 Jul;72(1):50-6. doi: 10.1111/j.1365-3083.2010.02406.x. PMID: 20591076
Lappalainen I, Ollila J, Smith CI, Vihinen M
Hum Mutat 1997;10(4):261-7. doi: 10.1002/(SICI)1098-1004(1997)10:4<261::AID-HUMU1>3.0.CO;2-K. PMID: 9338579

Diagnosis

Yazdani R, Fekrvand S, Shahkarami S, Azizi G, Moazzami B, Abolhassani H, Aghamohammadi A
Clin Immunol 2019 Jan;198:19-30. Epub 2018 Nov 13 doi: 10.1016/j.clim.2018.11.007. PMID: 30439505
Kanegane H, Hoshino A, Okano T, Yasumi T, Wada T, Takada H, Okada S, Yamashita M, Yeh TW, Nishikomori R, Takagi M, Imai K, Ochs HD, Morio T
Allergol Int 2018 Jan;67(1):43-54. Epub 2017 Jul 3 doi: 10.1016/j.alit.2017.06.003. PMID: 28684198
Qamar N, Fuleihan RL
Clin Rev Allergy Immunol 2014 Apr;46(2):120-30. doi: 10.1007/s12016-013-8378-7. PMID: 23797640
Kawai T, Nishikomori R, Heike T
Allergol Int 2012 Jun;61(2):207-17. doi: 10.2332/allergolint.12-RAI-0446. PMID: 22635013
Notarangelo LD, Duse M, Ugazio AG
Immunodefic Rev 1992;3(2):101-21. PMID: 1554497

Therapy

Huang SH, Meng XY, Bai ZJ, Li Y, Wu SY
J Trop Pediatr 2020 Dec 1;66(6):648-654. doi: 10.1093/tropej/fmaa023. PMID: 32388558
França TT, Barreiros LA, Al-Ramadi BK, Ochs HD, Cabral-Marques O, Condino-Neto A
Expert Rev Clin Immunol 2019 May;15(5):529-540. Epub 2019 Feb 18 doi: 10.1080/1744666X.2019.1573674. PMID: 30681380
Antachopoulos C
Clin Microbiol Infect 2010 Sep;16(9):1335-42. doi: 10.1111/j.1469-0691.2010.03289.x. PMID: 20840542
Buckley RH
Pediatr Clin North Am 1994 Aug;41(4):665-90. doi: 10.1016/s0031-3955(16)38803-4. PMID: 8047366
Notarangelo LD, Duse M, Ugazio AG
Immunodefic Rev 1992;3(2):101-21. PMID: 1554497

Prognosis

Yazdani R, Fekrvand S, Shahkarami S, Azizi G, Moazzami B, Abolhassani H, Aghamohammadi A
Clin Immunol 2019 Jan;198:19-30. Epub 2018 Nov 13 doi: 10.1016/j.clim.2018.11.007. PMID: 30439505
Nicolaides RE, de la Morena MT
Curr Opin Allergy Clin Immunol 2017 Dec;17(6):431-442. doi: 10.1097/ACI.0000000000000406. PMID: 29040209
Notarangelo LD, Hayward AR
Clin Exp Immunol 2000 Jun;120(3):399-405. doi: 10.1046/j.1365-2249.2000.01142.x. PMID: 10844515Free PMC Article
Notarangelo LD, Duse M, Ugazio AG
Immunodefic Rev 1992;3(2):101-21. PMID: 1554497
Schwaber J, Rosen FS
Immunodefic Rev 1990;2(3):233-51. PMID: 1981831

Clinical prediction guides

Pazhanisamy A, Jorge SD, Zimmermann MT, Kitcharoensakkul M, Abdalgani M, Khojah A, Victor C, Rueda C, Urrutia R, Abraham RS
Clin Immunol 2023 Aug;253:109692. Epub 2023 Jul 9 doi: 10.1016/j.clim.2023.109692. PMID: 37433422
Wang LL, Zhou W, Zhao W, Tian ZQ, Wang WF, Wang XF, Chen TX
J Immunol Res 2014;2014:683160. Epub 2014 Aug 20 doi: 10.1155/2014/683160. PMID: 25215306Free PMC Article
Madkaikar M, Gupta M, Chavan S, Italia K, Desai M, Merchant R, Radhakrishnan N, Ghosh K
Blood Cells Mol Dis 2014 Sep;53(3):99-104. Epub 2014 Jun 11 doi: 10.1016/j.bcmd.2014.05.008. PMID: 24929972
Antachopoulos C, Walsh TJ, Roilides E
Eur J Pediatr 2007 Nov;166(11):1099-117. Epub 2007 Jun 6 doi: 10.1007/s00431-007-0527-7. PMID: 17551753
Schwaber J, Rosen FS
Immunodefic Rev 1990;2(3):233-51. PMID: 1981831

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