Creutzfeldt-Jakob Syndrome
A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
Year introduced: 1991
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Subheadings:
Tree Number(s): C01.207.800.230, C10.228.140.380.165, C10.228.228.800.230, F03.615.400.300
MeSH Unique ID: D007562
Entry Terms:
- Creutzfeldt Jakob Syndrome
- Syndrome, Creutzfeldt-Jakob
- Jakob-Creutzfeldt Disease
- Disease, Jakob-Creutzfeldt
- Jakob Creutzfeldt Disease
- Jakob-Creutzfeldt Syndrome
- Jakob Creutzfeldt Syndrome
- Syndrome, Jakob-Creutzfeldt
- Creutzfeldt-Jakob Disease
- Creutzfeldt Jakob Disease
- Disease, Creutzfeldt-Jakob
- Spongiform Encephalopathy, Subacute
- Encephalopathies, Subacute Spongiform
- Encephalopathy, Subacute Spongiform
- Spongiform Encephalopathies, Subacute
- Subacute Spongiform Encephalopathies
- Subacute Spongiform Encephalopathy
- CJD (Creutzfeldt-Jakob Disease)
- CJD (Creutzfeldt Jakob Disease)
- Creutzfeldt Jacob Disease
- Disease, Creutzfeldt Jacob
- Jacob Disease, Creutzfeldt
- New Variant Creutzfeldt-Jakob Disease
- New Variant Creutzfeldt Jakob Disease
- V-CJD (Variant-Creutzfeldt-Jakob Disease)
- V CJD (Variant Creutzfeldt Jakob Disease)
- Creutzfeldt-Jakob Disease, New Variant
- Creutzfeldt Jakob Disease, New Variant
- Variant Creutzfeldt-Jakob Disease
- Variant Creutzfeldt Jakob Disease
- Creutzfeldt-Jakob Disease, Variant
- Creutzfeldt Jakob Disease, Variant
- Creutzfeldt-Jakob Disease, Familial
- Creutzfeldt Jakob Disease, Familial
- Creutzfeldt-Jakob Diseases, Familial
- Disease, Familial Creutzfeldt-Jakob
- Familial Creutzfeldt-Jakob Diseases
- Familial Creutzfeldt-Jakob Disease
- Familial Creutzfeldt Jakob Disease
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