Table 3. [Porphyria Classification Systems]. - GeneReviews®

Hereditary Porphyria	Primary Symptom-Based Porphyria Classification	Organ-Based Porphyria Classification
Acute intermittent porphyria (AIP)	Neurologic	Hepatic
ALA dehydratase deficiency porphyria (ADP)	Neurologic	Hepatic
Congenital erythropoietic porphyria (CEP)	Cutaneous	Erythropoietic
Erythropoietic protoporphyria (EPP)	Cutaneous	Erythropoietic
Hepatoerythropoietic porphyria (HEP)	Cutaneous	Hepatic/erythropoietic
Hereditary coproporphyria (HCP)	Neurologic (cutaneous possible but rare)	Hepatic
Porphyria cutanea tarda (PCT)	Cutaneous	Hepatic
Variegate porphyria (VP)	Cutaneous & neurologic	Hepatic
X-linked protoporphyria (XLP)	Cutaneous	Erythropoietic

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