Table 3.

Treatment of Manifestations in Individuals with Spinocerebellar Ataxia Type 38

Manifestation/
Concern
TreatmentConsiderations/Other
Ataxia Physical therapy to ameliorate coordination difficulties, especially w/walkingAlthough no clinical evidence of benefit has been offered thus far, individuals should maintain activity.
Crutches (less often canes) & walkersTo prevent falls
Home adaptations incl grab bars for bathtub or shower chairs, raised toilet seats, & ramps to accommodate motorized chairs, as needed
Dysarthria Speech-language therapyCommunication devices incl writing pads & computer-based devices may be of benefit.
Video esophagram can identify consistency of food least likely to trigger aspiration.Weighted eating utensils & dressing hooks help maintain a sense of independence.
Hearing loss Hearing aids may be helpful in selected cases.Consider referral to audiologist.
Anxiety Standard treatment
Family/
Community
  • Appropriate social work involvement to connect families w/local resources, respite, & support
  • Care coordination to manage multiple subspecialty appointments, equipment, medications, & supplies
Ongoing assessment for need of home nursing

From: Spinocerebellar Ataxia Type 38

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