Table 5. [Branchiooculofacial Syndrome: Recommended Surveillance]. - GeneReviews®

System/Concern	Evaluation	Frequency
Eyes/Vision	Ophthalmology exam & vision assessment	As recommended by ophthalmologist
Hearing	Audiology eval	As recommended by ENT/audiologist
Renal manifestations	Assess for recurrent urinary tract infections suggestive of vesicoureteral reflux.	At each visit
Dental	Teeth should be monitored for size & number, caries, & malocclusion.
Skin	Assess for new cysts.
Neurodevelopment/ Behavior/Psychiatric	Developmental & behavioral assessment	Annually or as needed
Monitor for signs of low self-esteem & other psychologic issues.	At each visit in older children as they enter adolescence

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