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Advanced Synovial Sarcoma

MedGen UID:
1666101
Concept ID:
C4727078
Neoplastic Process

Definition

A synovial sarcoma that has spread extensively to other anatomic sites or is no longer responding to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdvanced Synovial Sarcoma

Professional guidelines

PubMed

Kojima Y, Shimoi T, Seo T, Yazaki S, Okuya T, Ohtake Y, Okuma HS, Shimomura A, Nishikawa T, Tanioka M, Sudo K, Noguchi E, Tamura K, Yoshida A, Iwata S, Kobayashi E, Kawai A, Fujiwara Y, Yonemori K
Oncology 2022;100(7):370-375. Epub 2022 Apr 11 doi: 10.1159/000524500. PMID: 35405680
Ates O, Aksoy S, Yeter H, Sunar V, Kertmen N, Dizdar O, Turker A, Kars A
Indian J Cancer 2017 Jan-Mar;54(1):321-325. doi: 10.4103/ijc.IJC_169_17. PMID: 29199714
Do K, Doroshow JH, Kummar S
Curr Opin Oncol 2012 Jul;24(4):425-30. doi: 10.1097/CCO.0b013e328354c141. PMID: 22572725Free PMC Article

Recent clinical studies

Etiology

Tansir G, Rastogi S, Kumar A, Barwad A, Mridha AR, Dhamija E, Shamim SA, Bhatnagar S, Bhoriwal S
BMC Cancer 2023 Jul 8;23(1):639. doi: 10.1186/s12885-023-11099-4. PMID: 37422615Free PMC Article
Scheer M, Hallmen E, Vokuhl C, Fuchs J, Tunn PU, Münter M, Timmermann B, Bauer S, Henssen AG, Kazanowska B, Niggli F, Ladenstein R, Ljungman G, Eggert A, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe [CWS]
J Cancer Res Clin Oncol 2023 May;149(5):1717-1731. Epub 2022 Jun 10 doi: 10.1007/s00432-022-04051-9. PMID: 35687182Free PMC Article
Kojima Y, Shimoi T, Seo T, Yazaki S, Okuya T, Ohtake Y, Okuma HS, Shimomura A, Nishikawa T, Tanioka M, Sudo K, Noguchi E, Tamura K, Yoshida A, Iwata S, Kobayashi E, Kawai A, Fujiwara Y, Yonemori K
Oncology 2022;100(7):370-375. Epub 2022 Apr 11 doi: 10.1159/000524500. PMID: 35405680
Ates O, Aksoy S, Yeter H, Sunar V, Kertmen N, Dizdar O, Turker A, Kars A
Indian J Cancer 2017 Jan-Mar;54(1):321-325. doi: 10.4103/ijc.IJC_169_17. PMID: 29199714
Palmerini E, Paioli A, Ferrari S
Expert Rev Anticancer Ther 2014 Jul;14(7):791-806. Epub 2014 Mar 24 doi: 10.1586/14737140.2014.901155. PMID: 24661286

Diagnosis

Scheer M, Hallmen E, Vokuhl C, Fuchs J, Tunn PU, Münter M, Timmermann B, Bauer S, Henssen AG, Kazanowska B, Niggli F, Ladenstein R, Ljungman G, Eggert A, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe [CWS]
J Cancer Res Clin Oncol 2023 May;149(5):1717-1731. Epub 2022 Jun 10 doi: 10.1007/s00432-022-04051-9. PMID: 35687182Free PMC Article
Chen S, Zhang K, Wan X, Chen Y, Ma S, Deng Q
Medicine (Baltimore) 2019 Dec;98(51):e18382. doi: 10.1097/MD.0000000000018382. PMID: 31861000Free PMC Article
Ates O, Aksoy S, Yeter H, Sunar V, Kertmen N, Dizdar O, Turker A, Kars A
Indian J Cancer 2017 Jan-Mar;54(1):321-325. doi: 10.4103/ijc.IJC_169_17. PMID: 29199714
Yetisyigit T, Arpaci E, Seber ES, Kucukoner M, Kos FT, Sonmez OU, Alici S, Akman T, Aktas B, Yildiz R, Gunaydin Y, Inanc M, Demirci U, Alkis N, Gumus M
Asian Pac J Cancer Prev 2013;14(9):5185-8. doi: 10.7314/apjcp.2013.14.9.5185. PMID: 24175798
Spurrell EL, Fisher C, Thomas JM, Judson IR
Ann Oncol 2005 Mar;16(3):437-44. Epub 2005 Jan 14 doi: 10.1093/annonc/mdi082. PMID: 15653701

Therapy

D'Angelo SP, Araujo DM, Abdul Razak AR, Agulnik M, Attia S, Blay JY, Carrasco Garcia I, Charlson JA, Choy E, Demetri GD, Druta M, Forcade E, Ganjoo KN, Glod J, Keedy VL, Le Cesne A, Liebner DA, Moreno V, Pollack SM, Schuetze SM, Schwartz GK, Strauss SJ, Tap WD, Thistlethwaite F, Valverde Morales CM, Wagner MJ, Wilky BA, McAlpine C, Hudson L, Navenot JM, Wang T, Bai J, Rafail S, Wang R, Sun A, Fernandes L, Van Winkle E, Elefant E, Lunt C, Norry E, Williams D, Biswas S, Van Tine BA
Lancet 2024 Apr 13;403(10435):1460-1471. Epub 2024 Mar 27 doi: 10.1016/S0140-6736(24)00319-2. PMID: 38554725
Tansir G, Rastogi S, Kumar A, Barwad A, Mridha AR, Dhamija E, Shamim SA, Bhatnagar S, Bhoriwal S
BMC Cancer 2023 Jul 8;23(1):639. doi: 10.1186/s12885-023-11099-4. PMID: 37422615Free PMC Article
Kojima Y, Shimoi T, Seo T, Yazaki S, Okuya T, Ohtake Y, Okuma HS, Shimomura A, Nishikawa T, Tanioka M, Sudo K, Noguchi E, Tamura K, Yoshida A, Iwata S, Kobayashi E, Kawai A, Fujiwara Y, Yonemori K
Oncology 2022;100(7):370-375. Epub 2022 Apr 11 doi: 10.1159/000524500. PMID: 35405680
Ates O, Aksoy S, Yeter H, Sunar V, Kertmen N, Dizdar O, Turker A, Kars A
Indian J Cancer 2017 Jan-Mar;54(1):321-325. doi: 10.4103/ijc.IJC_169_17. PMID: 29199714
Palmerini E, Paioli A, Ferrari S
Expert Rev Anticancer Ther 2014 Jul;14(7):791-806. Epub 2014 Mar 24 doi: 10.1586/14737140.2014.901155. PMID: 24661286

Prognosis

Scheer M, Hallmen E, Vokuhl C, Fuchs J, Tunn PU, Münter M, Timmermann B, Bauer S, Henssen AG, Kazanowska B, Niggli F, Ladenstein R, Ljungman G, Eggert A, Klingebiel T, Koscielniak E; Cooperative Weichteilsarkom Studiengruppe [CWS]
J Cancer Res Clin Oncol 2023 May;149(5):1717-1731. Epub 2022 Jun 10 doi: 10.1007/s00432-022-04051-9. PMID: 35687182Free PMC Article
Kogushi K, LoPresti M, Ikeda S
Future Oncol 2020 Dec;16(35):2997-3013. Epub 2020 Aug 27 doi: 10.2217/fon-2020-0575. PMID: 32851862
Ates O, Aksoy S, Yeter H, Sunar V, Kertmen N, Dizdar O, Turker A, Kars A
Indian J Cancer 2017 Jan-Mar;54(1):321-325. doi: 10.4103/ijc.IJC_169_17. PMID: 29199714
Yetisyigit T, Arpaci E, Seber ES, Kucukoner M, Kos FT, Sonmez OU, Alici S, Akman T, Aktas B, Yildiz R, Gunaydin Y, Inanc M, Demirci U, Alkis N, Gumus M
Asian Pac J Cancer Prev 2013;14(9):5185-8. doi: 10.7314/apjcp.2013.14.9.5185. PMID: 24175798
Do K, Doroshow JH, Kummar S
Curr Opin Oncol 2012 Jul;24(4):425-30. doi: 10.1097/CCO.0b013e328354c141. PMID: 22572725Free PMC Article

Clinical prediction guides

Chen S, Zhang K, Wan X, Chen Y, Ma S, Deng Q
Medicine (Baltimore) 2019 Dec;98(51):e18382. doi: 10.1097/MD.0000000000018382. PMID: 31861000Free PMC Article
Ramachandran I, Lowther DE, Dryer-Minnerly R, Wang R, Fayngerts S, Nunez D, Betts G, Bath N, Tipping AJ, Melchiori L, Navenot JM, Glod J, Mackall CL, D'Angelo SP, Araujo DM, Chow WA, Demetri GD, Druta M, Van Tine BA, Grupp SA, Abdul Razak AR, Wilky B, Iyengar M, Trivedi T, Winkle EV, Chagin K, Amado R, Binder GK, Basu S
J Immunother Cancer 2019 Oct 24;7(1):276. doi: 10.1186/s40425-019-0762-2. PMID: 31651363Free PMC Article
Ates O, Aksoy S, Yeter H, Sunar V, Kertmen N, Dizdar O, Turker A, Kars A
Indian J Cancer 2017 Jan-Mar;54(1):321-325. doi: 10.4103/ijc.IJC_169_17. PMID: 29199714
Vlenterie M, Litière S, Rizzo E, Marréaud S, Judson I, Gelderblom H, Le Cesne A, Wardelmann E, Messiou C, Gronchi A, van der Graaf WT
Eur J Cancer 2016 May;58:62-72. Epub 2016 Mar 8 doi: 10.1016/j.ejca.2016.02.002. PMID: 26968015
Spurrell EL, Fisher C, Thomas JM, Judson IR
Ann Oncol 2005 Mar;16(3):437-44. Epub 2005 Jan 14 doi: 10.1093/annonc/mdi082. PMID: 15653701

Recent systematic reviews

Kogushi K, LoPresti M, Ikeda S
Future Oncol 2020 Dec;16(35):2997-3013. Epub 2020 Aug 27 doi: 10.2217/fon-2020-0575. PMID: 32851862

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