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Lymphatic vessel neoplasm

MedGen UID:
64616
•Concept ID:
C0206619
•
Neoplastic Process
Synonyms: Lymphatic Vessel Tumor; Lymphatic Vessel Tumors; Tumor, Lymphatic Vessel; Tumors, Lymphatic Vessel
SNOMED CT: Lymphatic vessel tumor (115236002)
 
HPO: HP:0012797
Monarch Initiative: MONDO:0036870

Definition

A benign or malignant neoplasm arising from the lymphatic vessels. [from HPO]

Professional guidelines

PubMed

Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management.
McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX
Lancet Respir Med 2021 Nov;9(11):1313-1327. Epub 2021 Aug 27 doi: 10.1016/S2213-2600(21)00228-9. PMID: 34461049
Overview of primary adult retroperitoneal tumours.
Improta L, Tzanis D, Bouhadiba T, Abdelhafidh K, Bonvalot S
Eur J Surg Oncol 2020 Sep;46(9):1573-1579. Epub 2020 May 21 doi: 10.1016/j.ejso.2020.04.054. PMID: 32600897
Normalization of the vasculature for treatment of cancer and other diseases.
Goel S, Duda DG, Xu L, Munn LL, Boucher Y, Fukumura D, Jain RK
Physiol Rev 2011 Jul;91(3):1071-121. doi: 10.1152/physrev.00038.2010. PMID: 21742796Free PMC Article

Recent clinical studies

Etiology

Lymphangioleiomyomatosis.
Elia D, Cassandro R, Caminati A, Luisi F, Harari S
Presse Med 2023 Sep;52(3):104173. Epub 2023 Sep 9 doi: 10.1016/j.lpm.2023.104173. PMID: 37696446
Cystic lung disease.
Cabeza Martínez B, Giménez Palleiro A, Mazzini Florindez SP
Radiologia (Engl Ed) 2022 Dec;64 Suppl 3:265-276. doi: 10.1016/j.rxeng.2022.09.005. PMID: 36737165
Lymphatic and Mixed Malformations.
Hathaway BA, Radu S, Wilson J, Nauta AC
Lymphat Res Biol 2021 Feb;19(1):41-50. Epub 2021 Jan 25 doi: 10.1089/lrb.2020.0100. PMID: 33493408
Ultra-rare cystic disease.
Elia D, Torre O, Cassandro R, Caminati A, Harari S
Eur Respir Rev 2020 Sep 30;29(157) Epub 2020 Sep 2 doi: 10.1183/16000617.0163-2019. PMID: 32878971Free PMC Article
Lymphatic manifestations of lymphangioleiomyomatosis.
Gupta R, Kitaichi M, Inoue Y, Kotloff R, McCormack FX
Lymphology 2014 Sep;47(3):106-17. PMID: 25420303

Diagnosis

Stewart-Treves Syndrome.
Bernia E, Rios-Viñuela E, Requena C
JAMA Dermatol 2021 Jun 1;157(6):721. doi: 10.1001/jamadermatol.2021.0341. PMID: 33909015
Splenic lymphangioma.
Ioannidis I, Kahn AG
Arch Pathol Lab Med 2015 Feb;139(2):278-82. doi: 10.5858/arpa.2013-0656-RS. PMID: 25611113
A review of the management of lymphangiomas.
Ha J, Yu YC, Lannigan F
Curr Pediatr Rev 2014;10(3):238-48. doi: 10.2174/1573396309666131209210751. PMID: 25088344
Lymphangioleiomyomatosis.
Ansótegui Barrera E, Mancheño Franch N, Vera-Sempere F, Padilla Alarcón J
Arch Bronconeumol 2011 Feb;47(2):85-93. Epub 2011 Jan 20 doi: 10.1016/j.arbres.2010.08.008. PMID: 21255897
Gastric lymphangioma.
Kim HS, Lee SY, Lee YD, Kim DH, Kwon JG, Tak WY, Kweon YO, Kim SK, Choi YH, Chung JM
J Korean Med Sci 2001 Apr;16(2):229-32. doi: 10.3346/jkms.2001.16.2.229. PMID: 11306753Free PMC Article

Therapy

Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management.
McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX
Lancet Respir Med 2021 Nov;9(11):1313-1327. Epub 2021 Aug 27 doi: 10.1016/S2213-2600(21)00228-9. PMID: 34461049
Lymphangioleiomyomatosis.
Xu KF, Xu W, Liu S, Yu J, Tian X, Yang Y, Wang ST, Zhang W, Feng R, Zhang T
Semin Respir Crit Care Med 2020 Apr;41(2):256-268. Epub 2020 Apr 12 doi: 10.1055/s-0040-1702195. PMID: 32279296
Lymphangioleiomyomatosis (LAM).
Ataya A, Brantly M, Riley L
Am J Respir Crit Care Med 2018 Aug 15;198(4):P7-P8. doi: 10.1164/rccm.1984P7. PMID: 30109949
Lymphangioleiomyomatosis.
Sclafani A, VanderLaan P
N Engl J Med 2018 Jun 7;378(23):2224. doi: 10.1056/NEJMicm1712581. PMID: 29874537
Emerging biomarkers of lymphangioleiomyomatosis.
Nijmeh J, El-Chemaly S, Henske EP
Expert Rev Respir Med 2018 Feb;12(2):95-102. Epub 2017 Dec 1 doi: 10.1080/17476348.2018.1409622. PMID: 29171770

Prognosis

Lymphangioleiomyomatosis.
Doubková M, Štefániková M, Čan V, Merta Z, Svoboda M
Klin Onkol 2019 Fall;32(5):367-374. doi: 10.14735/amko2019367. PMID: 31610670
Splenic lymphangioma.
Ioannidis I, Kahn AG
Arch Pathol Lab Med 2015 Feb;139(2):278-82. doi: 10.5858/arpa.2013-0656-RS. PMID: 25611113
Lymphatic manifestations of lymphangioleiomyomatosis.
Gupta R, Kitaichi M, Inoue Y, Kotloff R, McCormack FX
Lymphology 2014 Sep;47(3):106-17. PMID: 25420303
Complex lymphatic anomalies.
Trenor CC 3rd, Chaudry G
Semin Pediatr Surg 2014 Aug;23(4):186-90. Epub 2014 Jul 22 doi: 10.1053/j.sempedsurg.2014.07.006. PMID: 25241096
Pancreatic hemolymphangioma.
Figueroa RM, Lopez GJ, Servin TE, Esquinca MH, Gómez-Pedraza A
JOP 2014 Jul 28;15(4):399-402. doi: 10.6092/1590-8577/2649. PMID: 25076353

Clinical prediction guides

Determinants of Progression and Mortality in Lymphangioleiomyomatosis.
Xu W, Yang C, Cheng C, Wang Y, Hu D, Huang J, He Y, Wang J, Chen K, Yang L, Zhou W, Zhang T, Liu S, Dai J, Meng S, Li X, Yang Y, Wang ST, Feng R, Zhang W, Zhang H, Wang L, Tian X, Xu KF
Chest 2023 Jul;164(1):137-148. Epub 2023 Feb 18 doi: 10.1016/j.chest.2023.02.026. PMID: 36801466
Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management.
McCarthy C, Gupta N, Johnson SR, Yu JJ, McCormack FX
Lancet Respir Med 2021 Nov;9(11):1313-1327. Epub 2021 Aug 27 doi: 10.1016/S2213-2600(21)00228-9. PMID: 34461049
Single-Cell Transcriptomic Analysis Identifies a Unique Pulmonary Lymphangioleiomyomatosis Cell.
Guo M, Yu JJ, Perl AK, Wikenheiser-Brokamp KA, Riccetti M, Zhang EY, Sudha P, Adam M, Potter A, Kopras EJ, Giannikou K, Potter SS, Sherman S, Hammes SR, Kwiatkowski DJ, Whitsett JA, McCormack FX, Xu Y
Am J Respir Crit Care Med 2020 Nov 15;202(10):1373-1387. doi: 10.1164/rccm.201912-2445OC. PMID: 32603599Free PMC Article
Lymphangioleiomyomatosis.
Doubková M, Štefániková M, Čan V, Merta Z, Svoboda M
Klin Onkol 2019 Fall;32(5):367-374. doi: 10.14735/amko2019367. PMID: 31610670
Complex lymphatic anomalies.
Trenor CC 3rd, Chaudry G
Semin Pediatr Surg 2014 Aug;23(4):186-90. Epub 2014 Jul 22 doi: 10.1053/j.sempedsurg.2014.07.006. PMID: 25241096

Recent systematic reviews

Traumatic subdural hygroma and chronic subdural hematoma: A systematic review and meta-analysis.
Yu J, Tang J, Chen M, Ren Q, He J, Tang M, Zhang X, Liu Z, Ding H
J Clin Neurosci 2023 Jan;107:23-33. Epub 2022 Nov 30 doi: 10.1016/j.jocn.2022.11.010. PMID: 36462413
Clinicopathological Features and Prognostic-Related Risk Factors of Gastric Signet Ring Cell Carcinoma: A Meta-Analysis.
Guo Y, Wang Q, Tian Q, Bo C, Li N, Zhang S, Li P
Comput Math Methods Med 2022;2022:3473445. Epub 2022 Aug 5 doi: 10.1155/2022/3473445. PMID: 36035278Free PMC Article
The prognostic influence of lymphatic endothelium-specific hyaluronan receptor 1 in cancer: A systematic review.
Karinen S, Hujanen R, Salo T, Salem A
Cancer Sci 2022 Jan;113(1):17-27. Epub 2021 Nov 24 doi: 10.1111/cas.15199. PMID: 34775672Free PMC Article
Interventions for orbital lymphangioma.
Patel SR, Rosenberg JB, Barmettler A
Cochrane Database Syst Rev 2019 May 15;5(5):CD013000. doi: 10.1002/14651858.CD013000.pub2. PMID: 31094450Free PMC Article
The role of lymphatic and blood vessel invasion in predicting survival and methods of detection in patients with primary operable breast cancer.
Gujam FJ, Going JJ, Edwards J, Mohammed ZM, McMillan DC
Crit Rev Oncol Hematol 2014 Feb;89(2):231-41. Epub 2013 Sep 12 doi: 10.1016/j.critrevonc.2013.08.014. PMID: 24075309

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