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Skin lymphangiosarcoma

MedGen UID:
87536
•Concept ID:
C0346082
•
Neoplastic Process
Synonyms: Angiosarcoma associated with chronic lymphedema; Lymphangiosarcoma following mastectomy; Postmastectomy extremity angiosarcoma; Stewart Treves syndrome
SNOMED CT: Stewart-Treves syndrome (62497000); Lymphangiosarcoma of Stewart and Treves (62497000); Lymphangiosarcoma of skin (62497000)
 
Monarch Initiative: MONDO:0021010

Definition

Lymphangiosarcoma occurring in patients with chronic lymphedema often following radical mastectomy but also reported in relation to congenital and other secondary forms of chronic lymphedema. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSkin lymphangiosarcoma

Professional guidelines

PubMed

Kaposi Sarcoma and Cutaneous Angiosarcoma: Guidelines for Diagnosis and Treatment.
Requena C, Alsina M, Morgado-Carrasco D, Cruz J, Sanmartín O, Serra-Guillén C, Llombart B
Actas Dermosifiliogr (Engl Ed) 2018 Dec;109(10):878-887. Epub 2018 Sep 24 doi: 10.1016/j.ad.2018.06.013. PMID: 30262126
The integrated and interdisciplinary treatment of chronic lymphedema.
Doś J, Górska-Doś M, Szuba A
Rocz Akad Med Bialymst 2005;50 Suppl 1:141-4. PMID: 16119649
Vascular and lymphatic tumors in infancy, childhood and adulthood: challenge of diagnosis and treatment.
Edgerton MT, Hiebert JM
Curr Probl Cancer 1978 Jan;2(7):1-44. doi: 10.1016/s0147-0272(78)80001-4. PMID: 373997

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