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Benign peripheral nerve sheath tumor

MedGen UID:
1843306
Concept ID:
C5577926
Neoplastic Process
Synonyms: benign peripheral nerve sheath tumor; BPNST
 
Monarch Initiative: MONDO:0016752
Orphanet: ORPHA252131

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVBenign peripheral nerve sheath tumor

Professional guidelines

PubMed

Ferner RE, Gutmann DH
Handb Clin Neurol 2013;115:939-55. doi: 10.1016/B978-0-444-52902-2.00053-9. PMID: 23931823

Recent clinical studies

Etiology

Hu XB, Gu C, Chen AQ, Ying GY, Shen F, Zhu YJ
Oper Neurosurg (Hagerstown) 2023 May 1;24(5):483-491. Epub 2023 Jan 26 doi: 10.1227/ons.0000000000000570. PMID: 36735518
Lee SK, Kim JY, Jeong HS
PLoS One 2020;15(3):e0230816. Epub 2020 Mar 26 doi: 10.1371/journal.pone.0230816. PMID: 32214392Free PMC Article
Stone JJ, Boland JM, Spinner RJ
World Neurosurg 2018 Nov;119:e986-e990. Epub 2018 Aug 13 doi: 10.1016/j.wneu.2018.08.022. PMID: 30114537
Georgescu TA, Dumitru AV, Oproiu AM, Nica AE, Costache D, Pătraşcu OM, Lăzăroiu AM, Chefani AE, Sajin M, Costache M
Rom J Morphol Embryol 2018;59(1):303-309. PMID: 29940642
James AW, Shurell E, Singh A, Dry SM, Eilber FC
Surg Oncol Clin N Am 2016 Oct;25(4):789-802. doi: 10.1016/j.soc.2016.05.009. PMID: 27591499

Diagnosis

Uerschels AK, Dengler NF, Chihi M, Lenkeit A, Dinger TF, Jabbarli R, Sure U, Hagenacker T, Wrede KH, Gembruch O
Neurosurg Rev 2023 Aug 18;46(1):205. doi: 10.1007/s10143-023-02107-z. PMID: 37594583Free PMC Article
Schadel CM, Anderson CW, Chi AC, Steed MB
J Oral Maxillofac Surg 2019 Feb;77(2):329.e1-329.e7. Epub 2018 Oct 4 doi: 10.1016/j.joms.2018.09.032. PMID: 30712535
Larque AB, Bredella MA, Nielsen GP, Chebib I
Skeletal Radiol 2017 Nov;46(11):1463-1468. Epub 2017 Jul 8 doi: 10.1007/s00256-017-2710-x. PMID: 28689338
James AW, Shurell E, Singh A, Dry SM, Eilber FC
Surg Oncol Clin N Am 2016 Oct;25(4):789-802. doi: 10.1016/j.soc.2016.05.009. PMID: 27591499
Ferner RE, Gutmann DH
Handb Clin Neurol 2013;115:939-55. doi: 10.1016/B978-0-444-52902-2.00053-9. PMID: 23931823

Therapy

Jain PV, Squires C, Gasparri M, Sheinin Y
Ann Diagn Pathol 2022 Apr;57:151880. Epub 2021 Dec 27 doi: 10.1016/j.anndiagpath.2021.151880. PMID: 34972037
Las Heras F, Martuza R, Caruso P, Rincon S, Stemmer-Rachamimov A
Brain Pathol 2013 May;23(3):361-2. doi: 10.1111/bpa.12055. PMID: 23587143Free PMC Article

Prognosis

Doğukan FM, Erdem ZB
Int J Surg Pathol 2023 Oct;31(7):1225-1231. Epub 2022 Dec 7 doi: 10.1177/10668969221143456. PMID: 36475929
Lau HD, Kong CS, Kao CS
Cancer Cytopathol 2018 Sep;126(9):782-796. Epub 2018 Sep 7 doi: 10.1002/cncy.22037. PMID: 30193011
Guha D, Davidson B, Nadi M, Alotaibi NM, Fehlings MG, Gentili F, Valiante TA, Tator CH, Tymianski M, Guha A, Zadeh G
J Neurosurg 2018 Apr;128(4):1226-1234. Epub 2017 Jul 7 doi: 10.3171/2017.1.JNS162292. PMID: 28686119
Iannaci G, Crispino M, Cifarelli P, Montella M, Panarese I, Ronchi A, Russo R, Tremiterra G, Luise R, Sapere P
World J Surg Oncol 2016 Feb 3;14(1):29. doi: 10.1186/s12957-016-0789-5. PMID: 26842370Free PMC Article
Pekmezci M, Reuss DE, Hirbe AC, Dahiya S, Gutmann DH, von Deimling A, Horvai AE, Perry A
Mod Pathol 2015 Feb;28(2):187-200. Epub 2014 Sep 5 doi: 10.1038/modpathol.2014.109. PMID: 25189642Free PMC Article

Clinical prediction guides

Doğukan FM, Erdem ZB
Int J Surg Pathol 2023 Oct;31(7):1225-1231. Epub 2022 Dec 7 doi: 10.1177/10668969221143456. PMID: 36475929
Lee SK, Kim JY, Jeong HS
PLoS One 2020;15(3):e0230816. Epub 2020 Mar 26 doi: 10.1371/journal.pone.0230816. PMID: 32214392Free PMC Article
Stone JJ, Spinner RJ
Oper Neurosurg (Hagerstown) 2020 Jan 1;18(1):60-68. doi: 10.1093/ons/opz034. PMID: 30888029
Guha D, Davidson B, Nadi M, Alotaibi NM, Fehlings MG, Gentili F, Valiante TA, Tator CH, Tymianski M, Guha A, Zadeh G
J Neurosurg 2018 Apr;128(4):1226-1234. Epub 2017 Jul 7 doi: 10.3171/2017.1.JNS162292. PMID: 28686119
Pekmezci M, Reuss DE, Hirbe AC, Dahiya S, Gutmann DH, von Deimling A, Horvai AE, Perry A
Mod Pathol 2015 Feb;28(2):187-200. Epub 2014 Sep 5 doi: 10.1038/modpathol.2014.109. PMID: 25189642Free PMC Article

Recent systematic reviews

Peraza Labrador AJ, Valdez LHM, Marin NRG, Ibazetta KAR, Villacis M, Chacon JL, Huaman HO, Pariahuamán HC, Angulo HB, Woo V
Head Neck Pathol 2023 Dec;17(4):984-999. Epub 2023 Dec 6 doi: 10.1007/s12105-023-01595-1. PMID: 38055108Free PMC Article
Martin E, Geitenbeek RTJ, Coert JH, Hanff DF, Graven LH, Grünhagen DJ, Verhoef C, Taal W
Neuro Oncol 2021 Apr 12;23(4):557-571. doi: 10.1093/neuonc/noaa280. PMID: 33326583Free PMC Article
Boyanton BL Jr, Jones JK, Shenaq SM, Hicks MJ, Bhattacharjee MB
Arch Pathol Lab Med 2007 Sep;131(9):1382-92. doi: 10.5858/2007-131-1382-IPASRW. PMID: 17824794

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