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Orbit Paraganglioma

MedGen UID:
235409
•Concept ID:
C1335130
•
Neoplastic Process
Synonyms: Orbital Paraganglioma; Paraganglioma of Orbit; Paraganglioma of the Orbit

Definition

An extra-adrenal paraganglioma arising from the orbit. Patients may present with visual disturbances or proptosis. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVOrbit Paraganglioma

Recent clinical studies

Etiology

Minimally Invasive 360-Degree Approach to Intraconal Orbital Tumors.
Caballero-García J, Aparicio-García C, Linares-Benavides YJ, López-Sánchez M, Abreu-Perdomo FA, Huanca-Amaru J
Am J Ophthalmol 2021 Apr;224:301-309. Epub 2020 Jul 30 doi: 10.1016/j.ajo.2020.07.035. PMID: 32738230
Orbital Paraganglioma.
Zhu B, Yan J
J Craniofac Surg 2019 Sep;30(6):e503-e506. doi: 10.1097/SCS.0000000000005408. PMID: 30896513
Neurofibromatosis type 1.
Gutmann DH, Ferner RE, Listernick RH, Korf BR, Wolters PL, Johnson KJ
Nat Rev Dis Primers 2017 Feb 23;3:17004. doi: 10.1038/nrdp.2017.4. PMID: 28230061
Paragangliomas of the head and neck.
Pellitteri PK, Rinaldo A, Myssiorek D, Gary Jackson C, Bradley PJ, Devaney KO, Shaha AR, Netterville JL, Manni JJ, Ferlito A
Oral Oncol 2004 Jul;40(6):563-75. doi: 10.1016/j.oraloncology.2003.09.004. PMID: 15063383
Extracranial sinonasal tract meningiomas: a clinicopathologic study of 30 cases with a review of the literature.
Thompson LD, Gyure KA
Am J Surg Pathol 2000 May;24(5):640-50. doi: 10.1097/00000478-200005000-00002. PMID: 10800982

Diagnosis

Orbital Paraganglioma.
Zhu B, Yan J
J Craniofac Surg 2019 Sep;30(6):e503-e506. doi: 10.1097/SCS.0000000000005408. PMID: 30896513
Neurofibromatosis type 1.
Gutmann DH, Ferner RE, Listernick RH, Korf BR, Wolters PL, Johnson KJ
Nat Rev Dis Primers 2017 Feb 23;3:17004. doi: 10.1038/nrdp.2017.4. PMID: 28230061
Paragangliomas of the head and neck.
Pellitteri PK, Rinaldo A, Myssiorek D, Gary Jackson C, Bradley PJ, Devaney KO, Shaha AR, Netterville JL, Manni JJ, Ferlito A
Oral Oncol 2004 Jul;40(6):563-75. doi: 10.1016/j.oraloncology.2003.09.004. PMID: 15063383
Extracranial sinonasal tract meningiomas: a clinicopathologic study of 30 cases with a review of the literature.
Thompson LD, Gyure KA
Am J Surg Pathol 2000 May;24(5):640-50. doi: 10.1097/00000478-200005000-00002. PMID: 10800982
Glomus bodies and tumors.
Lawson W
N Y State J Med 1980 Sep;80(10):1567-75. PMID: 6252521

Therapy

Visual Outcomes After Endoscopic Endonasal Resection of Orbital Lesions.
Yang K, Ellenbogen Y, Algird AR, Sommer DD, Reddy K
World Neurosurg 2020 Jul;139:e501-e507. Epub 2020 Apr 18 doi: 10.1016/j.wneu.2020.04.050. PMID: 32311560
Pheochromocytoma Multisystem Crisis Triggered by Glucocorticoid Administration and Aggravated by Citrate Dialysis.
Yeoh CJ, Ng SY, Goh BK
A A Case Rep 2017 Feb 1;8(3):58-60. doi: 10.1213/XAA.0000000000000423. PMID: 27828782

Prognosis

Visual Outcomes After Endoscopic Endonasal Resection of Orbital Lesions.
Yang K, Ellenbogen Y, Algird AR, Sommer DD, Reddy K
World Neurosurg 2020 Jul;139:e501-e507. Epub 2020 Apr 18 doi: 10.1016/j.wneu.2020.04.050. PMID: 32311560
Head and neck paragangliomas: an overview.
Myssiorek D
Otolaryngol Clin North Am 2001 Oct;34(5):829-36, v. doi: 10.1016/s0030-6665(05)70349-2. PMID: 11557441
Extracranial sinonasal tract meningiomas: a clinicopathologic study of 30 cases with a review of the literature.
Thompson LD, Gyure KA
Am J Surg Pathol 2000 May;24(5):640-50. doi: 10.1097/00000478-200005000-00002. PMID: 10800982
Malignant paraganglioma of frontoethmoidal region.
Sharma HS, Madhavan M, Othman NH, Muhamad M, Abdullah JM
Auris Nasus Larynx 1999 Oct;26(4):487-93. doi: 10.1016/s0385-8146(99)00030-9. PMID: 10530746
Neurogenic tumors of the orbit.
Günalp I, Gündüz K, Dürük K, Kanpolat Y
Jpn J Ophthalmol 1994;38(2):185-90. PMID: 7967211

Clinical prediction guides

Orbital Paraganglioma.
Zhu B, Yan J
J Craniofac Surg 2019 Sep;30(6):e503-e506. doi: 10.1097/SCS.0000000000005408. PMID: 30896513
Orbital Paraganglioma in Infancy: Does It Behave More Aggressively?
Khatri D, Das KK, Jaiswal A, Kumar R, Jaiswal S
World Neurosurg 2018 Aug;116:242-246. Epub 2018 May 29 doi: 10.1016/j.wneu.2018.05.146. PMID: 29857209
Regression of a paraganglioma tumor of the orbit.
Hill RH 3rd, Platt SM, Bersani TA, Barker-Griffith A, Strumpf KB
Orbit 2015 Apr;34(2):99-102. Epub 2014 Sep 12 doi: 10.3109/01676830.2014.950290. PMID: 25216041
CyberKnife Frameless Radiosurgery for the treatment of extracranial benign tumors.
Bhatnagar AK, Gerszten PC, Ozhasaglu C, Vogel WJ, Kalnicki S, Welch WC, Burton SA
Technol Cancer Res Treat 2005 Oct;4(5):571-6. doi: 10.1177/153303460500400511. PMID: 16173828
Paragangliomas of the head and neck region: a clinical study of 69 patients.
Lack EE, Cubilla AL, Woodruff JM, Farr HW
Cancer 1977 Feb;39(2):397-409. doi: 10.1002/1097-0142(197702)39:2<397::aid-cncr2820390205>3.0.co;2-c. PMID: 837327

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